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- Glycogen_storage_disease_type_VI abstract "Glycogen storage disease type VI (GSD VI) is a type of glycogen storage disease caused by a deficiency in liver glycogen phosphorylase or other components of the associated phosphorylase cascade system.It is also known as \"Hers' disease\", after Henri G. Hers, who characterized it in 1959.The scope of GSD VI now also includes glycogen storage disease type VIII, IX (caused by phosphorylase b kinase deficiency) and X (deficiency of protein kinase A). These were previously considered to be distinct GSD types.The incidence of GSD VI is approximately 1 case per 65,000–85,000 births, representing approximately 30% all cases of glycogen storage disease. Approximately 75% of these GSD VI cases result from the X-linked recessive forms of phosphorylase kinase deficiency. All other forms are autosomal recessive.".
- Glycogen_storage_disease_type_VI icd10 "E74.0".
- Glycogen_storage_disease_type_VI icd9 "271.0".
- Glycogen_storage_disease_type_VI meshId "D006013".
- Glycogen_storage_disease_type_VI omim "232700".
- Glycogen_storage_disease_type_VI thumbnail Glycogen.png?width=300.
- Glycogen_storage_disease_type_VI wikiPageExternalLink default.asp.
- Glycogen_storage_disease_type_VI wikiPageExternalLink NBK5941.
- Glycogen_storage_disease_type_VI wikiPageID "10263466".
- Glycogen_storage_disease_type_VI wikiPageLength "3377".
- Glycogen_storage_disease_type_VI wikiPageOutDegree "18".
- Glycogen_storage_disease_type_VI wikiPageRevisionID "609505893".
- Glycogen_storage_disease_type_VI wikiPageWikiLink Category:Inborn_errors_of_carbohydrate_metabolism.
- Glycogen_storage_disease_type_VI wikiPageWikiLink Delayed_milestone.
- Glycogen_storage_disease_type_VI wikiPageWikiLink Dominance_(genetics).
- Glycogen_storage_disease_type_VI wikiPageWikiLink Glycogen.
- Glycogen_storage_disease_type_VI wikiPageWikiLink Glycogen_phosphorylase.
- Glycogen_storage_disease_type_VI wikiPageWikiLink Glycogen_storage_disease.
- Glycogen_storage_disease_type_VI wikiPageWikiLink Henri_G._Hers.
- Glycogen_storage_disease_type_VI wikiPageWikiLink Hepatomegaly.
- Glycogen_storage_disease_type_VI wikiPageWikiLink Hyperlipidemia.
- Glycogen_storage_disease_type_VI wikiPageWikiLink Hypoglycemia.
- Glycogen_storage_disease_type_VI wikiPageWikiLink Ketosis.
- Glycogen_storage_disease_type_VI wikiPageWikiLink Lactic_acid.
- Glycogen_storage_disease_type_VI wikiPageWikiLink Phosphorylase_kinase.
- Glycogen_storage_disease_type_VI wikiPageWikiLink Protein_kinase_A.
- Glycogen_storage_disease_type_VI wikiPageWikiLink Uric_acid.
- Glycogen_storage_disease_type_VI wikiPageWikiLink X-linked_recessive_inheritance.
- Glycogen_storage_disease_type_VI wikiPageWikiLinkText "GSD type VI".
- Glycogen_storage_disease_type_VI wikiPageWikiLinkText "Glycogen storage disease type VI".
- Glycogen_storage_disease_type_VI wikiPageWikiLinkText "glycogen storage disease type VI".
- Glycogen_storage_disease_type_VI wikiPageWikiLinkText "glycogen storage diseases VIII, IX, X".
- Glycogen_storage_disease_type_VI caption Glycogen.
- Glycogen_storage_disease_type_VI diseasesdb "5311".
- Glycogen_storage_disease_type_VI emedicinesubj "med".
- Glycogen_storage_disease_type_VI emedicinetopic "912".
- Glycogen_storage_disease_type_VI genereviewsname "Glycogen Storage Disease Type VI".
- Glycogen_storage_disease_type_VI genereviewsnbk "NBK5941".
- Glycogen_storage_disease_type_VI icd "271".
- Glycogen_storage_disease_type_VI icd "E74.0".
- Glycogen_storage_disease_type_VI meshid "D006013".
- Glycogen_storage_disease_type_VI name "Glycogen storage disease type VI".
- Glycogen_storage_disease_type_VI omim "232700".
- Glycogen_storage_disease_type_VI wikiPageUsesTemplate Template:Carbohydrate_metabolic_pathology.
- Glycogen_storage_disease_type_VI wikiPageUsesTemplate Template:EMedicine2.
- Glycogen_storage_disease_type_VI wikiPageUsesTemplate Template:Endocrine-disease-stub.
- Glycogen_storage_disease_type_VI wikiPageUsesTemplate Template:Infobox_disease.
- Glycogen_storage_disease_type_VI wikiPageUsesTemplate Template:Reflist.
- Glycogen_storage_disease_type_VI subject Category:Inborn_errors_of_carbohydrate_metabolism.
- Glycogen_storage_disease_type_VI hypernym Disease.
- Glycogen_storage_disease_type_VI type Disease.
- Glycogen_storage_disease_type_VI type Error.
- Glycogen_storage_disease_type_VI type Redirect.
- Glycogen_storage_disease_type_VI type Thing.
- Glycogen_storage_disease_type_VI type Q12136.
- Glycogen_storage_disease_type_VI comment "Glycogen storage disease type VI (GSD VI) is a type of glycogen storage disease caused by a deficiency in liver glycogen phosphorylase or other components of the associated phosphorylase cascade system.It is also known as \"Hers' disease\", after Henri G. Hers, who characterized it in 1959.The scope of GSD VI now also includes glycogen storage disease type VIII, IX (caused by phosphorylase b kinase deficiency) and X (deficiency of protein kinase A).".
- Glycogen_storage_disease_type_VI label "Glycogen storage disease type VI".
- Glycogen_storage_disease_type_VI sameAs Q1947298.
- Glycogen_storage_disease_type_VI sameAs Morbus_Hers.
- Glycogen_storage_disease_type_VI sameAs Choroba_Hersa.
- Glycogen_storage_disease_type_VI sameAs m.02q6wlh.
- Glycogen_storage_disease_type_VI sameAs Болезнь_Герса.
- Glycogen_storage_disease_type_VI sameAs Q1947298.
- Glycogen_storage_disease_type_VI wasDerivedFrom Glycogen_storage_disease_type_VI?oldid=609505893.
- Glycogen_storage_disease_type_VI depiction Glycogen.png.
- Glycogen_storage_disease_type_VI isPrimaryTopicOf Glycogen_storage_disease_type_VI.
- Glycogen_storage_disease_type_VI name "Glycogen storage disease type VI".