Matches in DBpedia 2016-04 for { <http://dbpedia.org/resource/Factor_XIII_deficiency> ?p ?o }
Showing triples 1 to 50 of
50
with 100 triples per page.
- Factor_XIII_deficiency abstract "Factor XIII deficiency occurs exceedingly rarely, causing a severe bleeding tendency. The incidence is one in a million to one in five million people, with higher incidence in areas with consanguineous marriage such as Iran that has the highest global incidence of disorder. Most are due to mutations in the A subunit gene (located on chromosome 6p25-p24). This mutation is inherited in an autosomal recessive fashion.Deficiency of Factor XIII leads to defective cross-linking of fibrin and vulnerability to late re-bleeds when the primary hemostatic plug is overwhelmed. Bleeding tendencies similar to hemophiliacs develop, such as hemarthroses and deep tissue bleeding.As Factor XIII is composed of two subunit protein, A and B, for which the genes are located on different chromosomes, administration of recombinant A subunit improves clot stability and is becoming a therapeutic option for patients with this condition.".
- Factor_XIII_deficiency icd10 "D68.2".
- Factor_XIII_deficiency icd9 "286.3".
- Factor_XIII_deficiency meshId "D005177".
- Factor_XIII_deficiency omim "134570".
- Factor_XIII_deficiency wikiPageID "4304755".
- Factor_XIII_deficiency wikiPageLength "5600".
- Factor_XIII_deficiency wikiPageOutDegree "12".
- Factor_XIII_deficiency wikiPageRevisionID "705926531".
- Factor_XIII_deficiency wikiPageWikiLink Category:Coagulopathies.
- Factor_XIII_deficiency wikiPageWikiLink Category:Haemophilia.
- Factor_XIII_deficiency wikiPageWikiLink Factor_XIII.
- Factor_XIII_deficiency wikiPageWikiLink Fibrin.
- Factor_XIII_deficiency wikiPageWikiLink Fibrinolysis.
- Factor_XIII_deficiency wikiPageWikiLink Hemarthrosis.
- Factor_XIII_deficiency wikiPageWikiLink Homeostasis.
- Factor_XIII_deficiency wikiPageWikiLink Immunogenicity.
- Factor_XIII_deficiency wikiPageWikiLink Novo_Nordisk.
- Factor_XIII_deficiency wikiPageWikiLink Pharmacokinetics.
- Factor_XIII_deficiency wikiPageWikiLink Recombinant_DNA.
- Factor_XIII_deficiency wikiPageWikiLinkText "Factor XIII deficiency".
- Factor_XIII_deficiency wikiPageWikiLinkText "congenital deficiency".
- Factor_XIII_deficiency diseasesdb "31412".
- Factor_XIII_deficiency emedicinesubj "ped".
- Factor_XIII_deficiency emedicinetopic "3040".
- Factor_XIII_deficiency icd "286.3".
- Factor_XIII_deficiency icd "D68.2".
- Factor_XIII_deficiency meshid "D005177".
- Factor_XIII_deficiency name "Factor XIII deficiency".
- Factor_XIII_deficiency omim "134570".
- Factor_XIII_deficiency wikiPageUsesTemplate Template:Hematology.
- Factor_XIII_deficiency wikiPageUsesTemplate Template:Infobox_disease.
- Factor_XIII_deficiency wikiPageUsesTemplate Template:OMIM2.
- Factor_XIII_deficiency wikiPageUsesTemplate Template:Reflist.
- Factor_XIII_deficiency subject Category:Coagulopathies.
- Factor_XIII_deficiency subject Category:Haemophilia.
- Factor_XIII_deficiency type Disease.
- Factor_XIII_deficiency type Disorder.
- Factor_XIII_deficiency type Redirect.
- Factor_XIII_deficiency type Thing.
- Factor_XIII_deficiency type Q12136.
- Factor_XIII_deficiency comment "Factor XIII deficiency occurs exceedingly rarely, causing a severe bleeding tendency. The incidence is one in a million to one in five million people, with higher incidence in areas with consanguineous marriage such as Iran that has the highest global incidence of disorder. Most are due to mutations in the A subunit gene (located on chromosome 6p25-p24).".
- Factor_XIII_deficiency label "Factor XIII deficiency".
- Factor_XIII_deficiency sameAs Q1393725.
- Factor_XIII_deficiency sameAs Faktor-XIII-Mangel.
- Factor_XIII_deficiency sameAs m.02wvby0.
- Factor_XIII_deficiency sameAs Q1393725.
- Factor_XIII_deficiency wasDerivedFrom Factor_XIII_deficiency?oldid=705926531.
- Factor_XIII_deficiency isPrimaryTopicOf Factor_XIII_deficiency.
- Factor_XIII_deficiency name "Factor XIII deficiency".