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- Autoimmune_inner_ear_disease abstract "Autoimmune inner ear disease (AIED) was first defined by Dr. Brian McCabe in a landmark paper describing an autoimmune loss of hearing. The disease results in progressive sensorineural hearing loss (SNHL) that acts bilaterally and asymmetrically, and sometimes affects an individual's vestibular system. AIED is used to describe any disorder in which the inner ear is damaged as a result of an autoimmune response. Some examples of autoimmune disorders that have presented with AIED are Cogan's Syndrome, relapsing polychondritis, systemic lupus erythematosus, Wegener's granulomatosis, olyarteritis nodosa, Sjogren's syndrome, and Lyme disease.Research has come to the consensus that AIED is the result of antibodies or other immune cells that cause damage to structures of the inner ear such as the cochlea and vestibular system. Of note, AIED is the only known SNHL that responds to medical treatment, but withholding treatment for longer than three months may result in permanent hearing loss and the need for cochlear implant installation.Although AIED has been studied extensively over the past 25 years, no clear mechanism of pathogenesis has emerged. A recent paper performed a literature review of all relevant articles dating back to 1980, and proposed a mechanism of pathogenesis which includes an inflammatory response and immune cell attack on inner ear structures. This response leads to an over-activation of other immune cells such as T helper cells, resulting in vascular changes and cochlear harm. AIED appears to be a consequence of damaged sensorineural hearing due to electrochemical disturbances, microthrombosis, and immune cell deposition. Additionally, self-reactive antibodies and T-cells contribute to the aforementioned damage. Research has suggested a valuable next step in uncovering AIED pathogenesis is inquiry into the role of interleukin-1β (IL-1β).".
- Autoimmune_inner_ear_disease icd9 "388.8".
- Autoimmune_inner_ear_disease wikiPageID "18006163".
- Autoimmune_inner_ear_disease wikiPageLength "12398".
- Autoimmune_inner_ear_disease wikiPageOutDegree "27".
- Autoimmune_inner_ear_disease wikiPageRevisionID "707568385".
- Autoimmune_inner_ear_disease wikiPageWikiLink Antibody.
- Autoimmune_inner_ear_disease wikiPageWikiLink Audiometry.
- Autoimmune_inner_ear_disease wikiPageWikiLink Autoimmunity.
- Autoimmune_inner_ear_disease wikiPageWikiLink Category:Autoimmune_diseases.
- Autoimmune_inner_ear_disease wikiPageWikiLink Category:Diseases_of_the_ear_and_mastoid_process.
- Autoimmune_inner_ear_disease wikiPageWikiLink Cochlea.
- Autoimmune_inner_ear_disease wikiPageWikiLink Cochlear_implant.
- Autoimmune_inner_ear_disease wikiPageWikiLink Cogan_syndrome.
- Autoimmune_inner_ear_disease wikiPageWikiLink Corticosteroid.
- Autoimmune_inner_ear_disease wikiPageWikiLink Cross-reactivity.
- Autoimmune_inner_ear_disease wikiPageWikiLink Cyclophosphamide.
- Autoimmune_inner_ear_disease wikiPageWikiLink Electrocochleography.
- Autoimmune_inner_ear_disease wikiPageWikiLink Erythrocyte_sedimentation_rate.
- Autoimmune_inner_ear_disease wikiPageWikiLink Hsp70.
- Autoimmune_inner_ear_disease wikiPageWikiLink Infliximab.
- Autoimmune_inner_ear_disease wikiPageWikiLink Inner_ear.
- Autoimmune_inner_ear_disease wikiPageWikiLink Interleukin.
- Autoimmune_inner_ear_disease wikiPageWikiLink Lyme_disease.
- Autoimmune_inner_ear_disease wikiPageWikiLink Methotrexate.
- Autoimmune_inner_ear_disease wikiPageWikiLink Relapsing_polychondritis.
- Autoimmune_inner_ear_disease wikiPageWikiLink Rheumatoid_factor.
- Autoimmune_inner_ear_disease wikiPageWikiLink Sensorineural_hearing_loss.
- Autoimmune_inner_ear_disease wikiPageWikiLink Sjxc3xb6grens_syndrome.
- Autoimmune_inner_ear_disease wikiPageWikiLink T_cell.
- Autoimmune_inner_ear_disease wikiPageWikiLink T_helper_cell.
- Autoimmune_inner_ear_disease wikiPageWikiLink Tumor_necrosis_factor_alpha.
- Autoimmune_inner_ear_disease wikiPageWikiLink Vestibular_system.
- Autoimmune_inner_ear_disease wikiPageWikiLinkText "Autoimmune inner ear disease".
- Autoimmune_inner_ear_disease wikiPageWikiLinkText "Inner-ear Disease".
- Autoimmune_inner_ear_disease wikiPageWikiLinkText "autoimmune inner ear disease".
- Autoimmune_inner_ear_disease icd "388.8".
- Autoimmune_inner_ear_disease name "Autoimmune inner ear disease".
- Autoimmune_inner_ear_disease wikiPageUsesTemplate Template:Immunology-stub.
- Autoimmune_inner_ear_disease wikiPageUsesTemplate Template:Infobox_disease.
- Autoimmune_inner_ear_disease wikiPageUsesTemplate Template:Reflist.
- Autoimmune_inner_ear_disease subject Category:Autoimmune_diseases.
- Autoimmune_inner_ear_disease subject Category:Diseases_of_the_ear_and_mastoid_process.
- Autoimmune_inner_ear_disease type Disease.
- Autoimmune_inner_ear_disease type Disorder.
- Autoimmune_inner_ear_disease type Thing.
- Autoimmune_inner_ear_disease type Q12136.
- Autoimmune_inner_ear_disease comment "Autoimmune inner ear disease (AIED) was first defined by Dr. Brian McCabe in a landmark paper describing an autoimmune loss of hearing. The disease results in progressive sensorineural hearing loss (SNHL) that acts bilaterally and asymmetrically, and sometimes affects an individual's vestibular system. AIED is used to describe any disorder in which the inner ear is damaged as a result of an autoimmune response.".
- Autoimmune_inner_ear_disease label "Autoimmune inner ear disease".
- Autoimmune_inner_ear_disease sameAs Q4826344.
- Autoimmune_inner_ear_disease sameAs أمراض_الأذن_الداخلية_ذاتية_المناعة.
- Autoimmune_inner_ear_disease sameAs m.047tkvy.
- Autoimmune_inner_ear_disease sameAs Q4826344.
- Autoimmune_inner_ear_disease wasDerivedFrom Autoimmune_inner_ear_disease?oldid=707568385.
- Autoimmune_inner_ear_disease isPrimaryTopicOf Autoimmune_inner_ear_disease.
- Autoimmune_inner_ear_disease name "Autoimmune inner ear disease".