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- Multiple_endocrine_neoplasia_type_2b abstract "Multiple endocrine neoplasia type 2B (also known as "MEN2B", "Mucosal neuromata with endocrine tumors", "Multiple endocrine neoplasia type 3", and "Wagenmann–Froboese syndrome") is a genetic disease that causes multiple tumors on the mouth, eyes, and endocrine glands. It is the most severe type of multiple endocrine neoplasia, differentiated by the presence of benign oral and submucosal tumors in addition to endocrine malignancies. It was first described by Wagenmann in 1922, and was first recognized as a syndrome in 1965-1966 by E.D. Williams and D.J. Pollock.MEN 2B typically manifests before a child is 10 years old. Affected individuals tend to be tall and lanky, with an elongated face and protruding, blubbery lips. Benign tumors (neoplasms) develop in the mouth, eyes, and submucosa of almost all organs in the first decade of life.Medullary thyroid cancer almost always occurs, sometimes in infancy. It is often aggressive. Cancer of the adrenal glands (pheochromocytoma) occurs in 50% of cases.A variety of eponyms have been proposed for MEN 2B, such as Williams-Pollock syndrome, Gorlin-Vickers syndrome, and Wagenmann-Froboese syndrome. However, none ever gained sufficient traction to merit continued use, and are no longer used in the medical literature.The prevalence of MEN2B is not well established, but has been derived from other epidemiological considerations as 1 in 600,000 to 1 in 4,000,000. The annual incidence has been estimated at 4 per 100 million per year.".
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- Multiple_endocrine_neoplasia_type_2b omim "162300".
- Multiple_endocrine_neoplasia_type_2b thumbnail Medullary_thyroid_carcinoma_-_2_-_very_high_mag.jpg?width=300.
- Multiple_endocrine_neoplasia_type_2b wikiPageExternalLink www.amend.org.uk.
- Multiple_endocrine_neoplasia_type_2b wikiPageID "18031668".
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- Multiple_endocrine_neoplasia_type_2b wikiPageRevisionID "678976012".
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Abraham_Lincoln.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Adrenal_gland.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Alcian_blue.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Alcian_blue_stain.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink August_Wagenmann.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Autosomal_dominant.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Calcitonin.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Cancer.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Category:Autosomal_dominant_disorders.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Category:Endocrine-related_cutaneous_conditions.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Category:Endocrine_neoplasia.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Category:Hereditary_cancers.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Constipation.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Craniosynostosis.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink DNA_sequencing.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Dominance_(genetics).
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Edward_Baker_Lincoln.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Endocrine_system.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Eponym.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink H&E_stain.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Hyperplasia.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Hypotonia.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Luxol_fast_blue.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Luxol_fast_blue_stain.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Marfan_syndrome.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Medullary_carcinoma_of_the_thyroid.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Medullary_thyroid_cancer.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Metastasis.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Micrograph.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Multiple_endocrine_neoplasia.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Multiple_endocrine_neoplasia_type_1.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Multiple_endocrine_neoplasia_type_2.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Multiple_endocrine_neoplasia_type_2a.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Myelin.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Neoplasm.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Neuroma.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Perineurium.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Pheochromocytoma.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink RET_proto-oncogene.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Schwann_cell.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Sclera.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Stroma_(animal_tissue).
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Submucosa.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Tad_Lincoln.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Thyroidectomy.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Transforming_growth_factor_beta.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink Traumatic_neuroma.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLink William_Wallace_Lincoln.
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLinkText "MEN 2B".
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLinkText "MEN type 2b".
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLinkText "MEN2B".
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLinkText "MEN2b".
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLinkText "Multiple endocrine neoplasia type 2b".
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLinkText "Multiple endocrine neoplasia, type 2B".
- Multiple_endocrine_neoplasia_type_2b wikiPageWikiLinkText "multiple endocrine neoplasia type 2b".
- Multiple_endocrine_neoplasia_type_2b caption "Micrograph of medullary thyroid carcinoma, as may be seen in MEN 2b. H&E stain.".
- Multiple_endocrine_neoplasia_type_2b diseasesdb "22784".
- Multiple_endocrine_neoplasia_type_2b hasPhotoCollection Multiple_endocrine_neoplasia_type_2b.
- Multiple_endocrine_neoplasia_type_2b meshid "D018814".
- Multiple_endocrine_neoplasia_type_2b name "Multiple endocrine neoplasia type 2b".
- Multiple_endocrine_neoplasia_type_2b omim "162300".
- Multiple_endocrine_neoplasia_type_2b wikiPageUsesTemplate Template:Endocrine_gland_neoplasia.
- Multiple_endocrine_neoplasia_type_2b wikiPageUsesTemplate Template:Endocrine_pathology.
- Multiple_endocrine_neoplasia_type_2b wikiPageUsesTemplate Template:Infobox_disease.
- Multiple_endocrine_neoplasia_type_2b wikiPageUsesTemplate Template:Reflist.
- Multiple_endocrine_neoplasia_type_2b subject Category:Autosomal_dominant_disorders.
- Multiple_endocrine_neoplasia_type_2b subject Category:Endocrine-related_cutaneous_conditions.
- Multiple_endocrine_neoplasia_type_2b subject Category:Endocrine_neoplasia.
- Multiple_endocrine_neoplasia_type_2b subject Category:Hereditary_cancers.
- Multiple_endocrine_neoplasia_type_2b hypernym Disease.
- Multiple_endocrine_neoplasia_type_2b type Disease.
- Multiple_endocrine_neoplasia_type_2b type Type.
- Multiple_endocrine_neoplasia_type_2b type Disorder.
- Multiple_endocrine_neoplasia_type_2b type Type.
- Multiple_endocrine_neoplasia_type_2b type Thing.
- Multiple_endocrine_neoplasia_type_2b type Q12136.
- Multiple_endocrine_neoplasia_type_2b comment "Multiple endocrine neoplasia type 2B (also known as "MEN2B", "Mucosal neuromata with endocrine tumors", "Multiple endocrine neoplasia type 3", and "Wagenmann–Froboese syndrome") is a genetic disease that causes multiple tumors on the mouth, eyes, and endocrine glands. It is the most severe type of multiple endocrine neoplasia, differentiated by the presence of benign oral and submucosal tumors in addition to endocrine malignancies.".
- Multiple_endocrine_neoplasia_type_2b label "Multiple endocrine neoplasia type 2b".
- Multiple_endocrine_neoplasia_type_2b sameAs m.047nf8c.
- Multiple_endocrine_neoplasia_type_2b sameAs Множественная_эндокринная_неоплазия_типа_IIb.
- Multiple_endocrine_neoplasia_type_2b sameAs Множинна_ендокринна_неоплазія_тип_2Б.
- Multiple_endocrine_neoplasia_type_2b sameAs Q624748.
- Multiple_endocrine_neoplasia_type_2b sameAs Q624748.
- Multiple_endocrine_neoplasia_type_2b wasDerivedFrom Multiple_endocrine_neoplasia_type_2b?oldid=678976012.
- Multiple_endocrine_neoplasia_type_2b depiction Medullary_thyroid_carcinoma_-_2_-_very_high_mag.jpg.
- Multiple_endocrine_neoplasia_type_2b isPrimaryTopicOf Multiple_endocrine_neoplasia_type_2b.
- Multiple_endocrine_neoplasia_type_2b name "Multiple endocrine neoplasia type 2b".