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- Idiopathic_orbital_inflammatory_disease abstract "Idiopathic Orbital Inflammatory Disease, or orbital pseudotumor, refers to a marginated mass-like enhancing soft tissue involving any area of the orbit. It is the most common painful orbital mass in the adult population, and is associated with proptosis, cranial nerve palsy (Tolosa-Hunt syndrome), uveitis, and retinal detachment. Idiopathic orbital inflammatory syndrome, also known as orbital pseudotumor, was first described by Gleason in 1903 and by Busse and Hochhmein. It was then characterized as a distinct entity in 1905 by Birch-Hirschfeld. It is a benign, nongranulomatous orbital inflammatory process characterized by extraocular orbital and adnexal inflammation with no known local or systemic cause. Its diagnosis is of exclusion once neoplasm, primary infection and systemic disorders have been ruled-out. Once diagnosed, it is characterized by its chronicity, anatomic location or histologic subtype.Idiopathic orbital inflammation (IOI) has a varied clinical presentation depending on the involved tissue. It can range from a diffuse inflammatory process to a more localized inflammation of muscle, lacrimal gland or orbital fat. Its former name, orbital pseudotumor, is derived due to resemblance to a neoplasm. However, histologically it is characterized by inflammation. Although a benign condition, it may present with an aggressive clinical course with severe vision loss and oculomotor dysfunction.".
- Idiopathic_orbital_inflammatory_disease wikiPageID "27738398".
- Idiopathic_orbital_inflammatory_disease wikiPageLength "12690".
- Idiopathic_orbital_inflammatory_disease wikiPageOutDegree "14".
- Idiopathic_orbital_inflammatory_disease wikiPageRevisionID "673708923".
- Idiopathic_orbital_inflammatory_disease wikiPageWikiLink Carotid-cavernous_fistula.
- Idiopathic_orbital_inflammatory_disease wikiPageWikiLink Category:Diseases_of_the_eye_and_adnexa.
- Idiopathic_orbital_inflammatory_disease wikiPageWikiLink Category:IgG4-related_disease.
- Idiopathic_orbital_inflammatory_disease wikiPageWikiLink Cranial_nerve.
- Idiopathic_orbital_inflammatory_disease wikiPageWikiLink Cranial_nerves.
- Idiopathic_orbital_inflammatory_disease wikiPageWikiLink Exophthalmos.
- Idiopathic_orbital_inflammatory_disease wikiPageWikiLink Extraocular_muscles.
- Idiopathic_orbital_inflammatory_disease wikiPageWikiLink Granulomatosis_with_polyangiitis.
- Idiopathic_orbital_inflammatory_disease wikiPageWikiLink IgG4-related_ophthalmic_disease.
- Idiopathic_orbital_inflammatory_disease wikiPageWikiLink Orbital_cellulitis.
- Idiopathic_orbital_inflammatory_disease wikiPageWikiLink Proptosis.
- Idiopathic_orbital_inflammatory_disease wikiPageWikiLink Retinal_detachment.
- Idiopathic_orbital_inflammatory_disease wikiPageWikiLink Sarcoidosis.
- Idiopathic_orbital_inflammatory_disease wikiPageWikiLink Tolosa-Hunt_syndrome.
- Idiopathic_orbital_inflammatory_disease wikiPageWikiLink Tolosa–Hunt_syndrome.
- Idiopathic_orbital_inflammatory_disease wikiPageWikiLink Uveitis.
- Idiopathic_orbital_inflammatory_disease wikiPageWikiLink Wikt:palsy.
- Idiopathic_orbital_inflammatory_disease wikiPageWikiLinkText "Idiopathic orbital inflammatory disease".
- Idiopathic_orbital_inflammatory_disease wikiPageWikiLinkText "Orbital pseudotumor".
- Idiopathic_orbital_inflammatory_disease wikiPageWikiLinkText "idiopathic orbital inflammatory disease".
- Idiopathic_orbital_inflammatory_disease hasPhotoCollection Idiopathic_orbital_inflammatory_disease.
- Idiopathic_orbital_inflammatory_disease wikiPageUsesTemplate Template:Reflist.
- Idiopathic_orbital_inflammatory_disease subject Category:Diseases_of_the_eye_and_adnexa.
- Idiopathic_orbital_inflammatory_disease subject Category:IgG4-related_disease.
- Idiopathic_orbital_inflammatory_disease comment "Idiopathic Orbital Inflammatory Disease, or orbital pseudotumor, refers to a marginated mass-like enhancing soft tissue involving any area of the orbit. It is the most common painful orbital mass in the adult population, and is associated with proptosis, cranial nerve palsy (Tolosa-Hunt syndrome), uveitis, and retinal detachment. Idiopathic orbital inflammatory syndrome, also known as orbital pseudotumor, was first described by Gleason in 1903 and by Busse and Hochhmein.".
- Idiopathic_orbital_inflammatory_disease label "Idiopathic orbital inflammatory disease".
- Idiopathic_orbital_inflammatory_disease sameAs m.0cc807f.
- Idiopathic_orbital_inflammatory_disease sameAs Q5988889.
- Idiopathic_orbital_inflammatory_disease sameAs Q5988889.
- Idiopathic_orbital_inflammatory_disease wasDerivedFrom Idiopathic_orbital_inflammatory_disease?oldid=673708923.
- Idiopathic_orbital_inflammatory_disease isPrimaryTopicOf Idiopathic_orbital_inflammatory_disease.