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- Trimethylaminuria abstract "Trimethylaminuria (TMAU), as defined by the KIM consortium of endocrinology disorders as fish odor syndrome or fish malodor syndrome, is a rare metabolic disorder that causes a defect in the normal production of an enzyme named flavin-containing monooxygenase 3 (FMO3). When FMO3 is not working correctly or if not enough enzyme is produced, the body loses the ability to properly convert trimethylamine (TMA) from precursor compounds in food digestion into trimethylamine oxide (TMAO), through a process called N-oxygenation. Trimethylamine then builds up and is released in the person's sweat, urine, and breath, giving off a strong fishy odor or strong body odor. A variant of TMAU (secondary TMAU or TMAU2) exists where there is no genetic cause, yet excessive TMA is secreted, possibly due to intestinal dysbiosis, altered metabolism, or hormonal reasons.".
- Trimethylaminuria icd10 "E88.8".
- Trimethylaminuria icd9 "270.8".
- Trimethylaminuria omim "602079".
- Trimethylaminuria thumbnail Trimethylamine_chemical_structure.png?width=300.
- Trimethylaminuria wikiPageExternalLink www.genome.gov.
- Trimethylaminuria wikiPageExternalLink ghr.nlm.nih.gov.
- Trimethylaminuria wikiPageID "1620523".
- Trimethylaminuria wikiPageLength "10212".
- Trimethylaminuria wikiPageOutDegree "42".
- Trimethylaminuria wikiPageRevisionID "701053656".
- Trimethylaminuria wikiPageWikiLink Activated_carbon.
- Trimethylaminuria wikiPageWikiLink Bacterial_vaginosis.
- Trimethylaminuria wikiPageWikiLink Body_odor.
- Trimethylaminuria wikiPageWikiLink Carnitine.
- Trimethylaminuria wikiPageWikiLink Category:Autosomal_recessive_disorders.
- Trimethylaminuria wikiPageWikiLink Category:Inborn_errors_of_metabolism.
- Trimethylaminuria wikiPageWikiLink Cervical_cancer.
- Trimethylaminuria wikiPageWikiLink Chlorophyllin.
- Trimethylaminuria wikiPageWikiLink Choline.
- Trimethylaminuria wikiPageWikiLink Chromosome_1_(human).
- Trimethylaminuria wikiPageWikiLink Dominance_(genetics).
- Trimethylaminuria wikiPageWikiLink Egg_(food).
- Trimethylaminuria wikiPageWikiLink Enzyme.
- Trimethylaminuria wikiPageWikiLink False_positives_and_false_negatives.
- Trimethylaminuria wikiPageWikiLink File:Autorecessive.svg.
- Trimethylaminuria wikiPageWikiLink Flavin_containing_monooxygenase_3.
- Trimethylaminuria wikiPageWikiLink Gene.
- Trimethylaminuria wikiPageWikiLink Hepatitis.
- Trimethylaminuria wikiPageWikiLink Inborn_error_of_metabolism.
- Trimethylaminuria wikiPageWikiLink Lecithin.
- Trimethylaminuria wikiPageWikiLink Legume.
- Trimethylaminuria wikiPageWikiLink Liver.
- Trimethylaminuria wikiPageWikiLink Meat.
- Trimethylaminuria wikiPageWikiLink Metronidazole.
- Trimethylaminuria wikiPageWikiLink Missense_mutation.
- Trimethylaminuria wikiPageWikiLink Mutation.
- Trimethylaminuria wikiPageWikiLink Neomycin.
- Trimethylaminuria wikiPageWikiLink Nitrogen.
- Trimethylaminuria wikiPageWikiLink Nonsense_mutation.
- Trimethylaminuria wikiPageWikiLink Phenotype.
- Trimethylaminuria wikiPageWikiLink Progesterone.
- Trimethylaminuria wikiPageWikiLink Soybean.
- Trimethylaminuria wikiPageWikiLink Sulfur.
- Trimethylaminuria wikiPageWikiLink Trimethylamine.
- Trimethylaminuria wikiPageWikiLink Trimethylamine_N-oxide.
- Trimethylaminuria wikiPageWikiLink Urinary_tract_infection.
- Trimethylaminuria wikiPageWikiLinkText "Trimethylaminuria disorder".
- Trimethylaminuria wikiPageWikiLinkText "Trimethylaminuria".
- Trimethylaminuria wikiPageWikiLinkText "rare medical condition".
- Trimethylaminuria wikiPageWikiLinkText "trimethylaminuria disorder".
- Trimethylaminuria wikiPageWikiLinkText "trimethylaminuria".
- Trimethylaminuria caption Trimethylamine.
- Trimethylaminuria diseasesdb "4835".
- Trimethylaminuria genereviewsname "Trimethylaminuria".
- Trimethylaminuria genereviewsnbk "NBK1103".
- Trimethylaminuria icd "270.8".
- Trimethylaminuria icd "E88.8".
- Trimethylaminuria name "Trimethylaminuria".
- Trimethylaminuria omim "602079".
- Trimethylaminuria width "144".
- Trimethylaminuria wikiPageUsesTemplate Template:Amino_acid_metabolic_pathology.
- Trimethylaminuria wikiPageUsesTemplate Template:Infobox_disease.
- Trimethylaminuria wikiPageUsesTemplate Template:Reflist.
- Trimethylaminuria subject Category:Autosomal_recessive_disorders.
- Trimethylaminuria subject Category:Inborn_errors_of_metabolism.
- Trimethylaminuria hypernym Disorder.
- Trimethylaminuria type Disease.
- Trimethylaminuria type Defect.
- Trimethylaminuria type Disorder.
- Trimethylaminuria type Error.
- Trimethylaminuria type Pediatric.
- Trimethylaminuria type Thing.
- Trimethylaminuria type Q12136.
- Trimethylaminuria comment "Trimethylaminuria (TMAU), as defined by the KIM consortium of endocrinology disorders as fish odor syndrome or fish malodor syndrome, is a rare metabolic disorder that causes a defect in the normal production of an enzyme named flavin-containing monooxygenase 3 (FMO3).".
- Trimethylaminuria label "Trimethylaminuria".
- Trimethylaminuria sameAs Q506433.
- Trimethylaminuria sameAs بيلة_الثلاثي_ميثيل_امين.
- Trimethylaminuria sameAs Trimethylaminurie.
- Trimethylaminuria sameAs Trimetilaminuria.
- Trimethylaminuria sameAs Triméthylaminurie.
- Trimethylaminuria sameAs תסמונת_צחנת_הדג.
- Trimethylaminuria sameAs Trimetilaminuria.
- Trimethylaminuria sameAs トリメチルアミン尿症.
- Trimethylaminuria sameAs Trimethylaminurie.
- Trimethylaminuria sameAs Trimethylaminurie.
- Trimethylaminuria sameAs Trimetylaminuri.
- Trimethylaminuria sameAs Trimetyloaminuria.
- Trimethylaminuria sameAs Trimetilaminúria.
- Trimethylaminuria sameAs m.05h90t.
- Trimethylaminuria sameAs Триметиламинурия.
- Trimethylaminuria sameAs Trimetylaminuri.
- Trimethylaminuria sameAs மீன்_நெடிக்_கூட்டறிகுறி.
- Trimethylaminuria sameAs Trimethylaminuria.
- Trimethylaminuria sameAs Q506433.
- Trimethylaminuria wasDerivedFrom Trimethylaminuria?oldid=701053656.
- Trimethylaminuria depiction Trimethylamine_chemical_structure.png.
- Trimethylaminuria isPrimaryTopicOf Trimethylaminuria.
- Trimethylaminuria name "Trimethylaminuria".