Matches in DBpedia 2016-04 for { <http://dbpedia.org/resource/Thrombotic_thrombocytopenic_purpura> ?p ?o }
- Thrombotic_thrombocytopenic_purpura abstract "Thrombotic thrombocytopenic purpura (TTP or Moschcowitz syndrome) is a rare disorder of the blood-coagulation system, causing extensive microscopic clots to form in the small blood vessels throughout the body. These small blood clots, called thrombi, can damage many organs including the kidneys, heart and brain. In the era before effective treatment with plasma exchange, the fatality rate was about 90%. With plasma exchange, this has dropped to 10% at six months. Immunosuppressants, such as glucocorticoids, rituximab, cyclophosphamide, vincristine, or ciclosporin, may also be used if a relapse or recurrence follows plasma exchange.Most cases of TTP arise from inhibition of the enzyme ADAMTS13, a metalloprotease responsible for cleaving large multimers of von Willebrand factor (vWF) into smaller units, by autoantibodies. The increase in circulating multimers of vWF increase platelet adhesion to areas of endothelial injury, particularly at arteriole-capillary junctions.A rarer form of TTP, called Upshaw–Schulman syndrome, is genetically inherited as a dysfunction of ADAMTS13, resulting in persisting large vWF multimers.Red blood cells passing the microscopic clots are subjected to shear stress which damages their membranes, leading to rupture of red blood cells within blood vessels, which in turn leads to anaemia and schistocyte formation. Reduced blood flow due to thrombosis and cellular injury results in end organ damage. Current therapy is based on support and plasmapheresis to reduce circulating antibodies against ADAMTS13 and replenish blood levels of the enzyme.".
- Thrombotic_thrombocytopenic_purpura wikiPageID "472537".
- Thrombotic_thrombocytopenic_purpura wikiPageLength "26125".
- Thrombotic_thrombocytopenic_purpura wikiPageOutDegree "107".
- Thrombotic_thrombocytopenic_purpura wikiPageRevisionID "706993364".
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink ADAMTS13.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Aciclovir.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Acute_kidney_injury.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Anemia.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Antibody.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Aphasia.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Apheresis.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Arteriole.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Autoimmune_disease.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink B_cell.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Blood_film.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Blood_plasma.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Bruise.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink CD20.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Cancer.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Capillary.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Category:Autoimmune_diseases.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Category:Coagulopathies.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Category:Rare_diseases.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Category:Vascular-related_cutaneous_conditions.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Ciclosporin.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Circulatory_system.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Clopidogrel.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Coagulation.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Creatinine.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Cryosupernatant.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Cyclophosphamide.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Delirium.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Disseminated_disease.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Ecchymosis.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Eli_Moschcowitz.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink End_organ_damage.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Endothelium.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Enzyme.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Exchange_transfusion.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Fever.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Fresh_frozen_plasma.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Glucocorticoid.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Hallucination.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Headache.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Hematopoietic_stem_cell_transplantation.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Hematuria.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Hemolysis.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Hemolytic-uremic_syndrome.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Hypertension.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Immunosuppression.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Interferon.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Jaundice.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Lactate_dehydrogenase.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Malaise.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Metalloproteinase.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Microangiopathic_hemolytic_anemia.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Mitomycins.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Monoclonal_antibody.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Mount_Sinai_Beth_Israel.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Neurology.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink New_York_City.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Oxymorphone.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Petechia.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Pharmaceutical_drug.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Plasmapheresis.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Platelet.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Prasugrel.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Prednisolone.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Prednisone.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Pregnancy.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Presumptive_and_confirmatory_tests.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Protease.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Purpura.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Quinine.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Rare_disease.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Rituximab.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Schistocyte.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Shear_stress.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Splenectomy.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Stroke.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Subtypes_of_HIV.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Systemic_lupus_erythematosus.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Tacrolimus.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink The_New_England_Journal_of_Medicine.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Thrombocytopenia.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Thrombosis.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Thrombotic_microangiopathy.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Thrombus.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Ticlopidine.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Upshaw–Schulman_syndrome.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Vincristine.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLink Von_Willebrand_factor.
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLinkText "TTP".
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLinkText "Thrombotic thrombocytopenic purpura".
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLinkText "illness".
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLinkText "thrombotic thrombocytopenic purpura (TTP)".
- Thrombotic_thrombocytopenic_purpura wikiPageWikiLinkText "thrombotic thrombocytopenic purpura".
- Thrombotic_thrombocytopenic_purpura wikiPageUsesTemplate Template:Citation_needed.
- Thrombotic_thrombocytopenic_purpura wikiPageUsesTemplate Template:Diseases_of_the_skin_and_appendages_by_morphology.