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- SUCLA2 abstract "Succinyl-CoA ligase [ADP-forming] subunit beta, mitochondrial (SUCLA2), also known as ADP-forming succinyl-CoA synthetase (SCS-A), is an enzyme that in humans is encoded by the SUCLA2 gene on chromosome 13.Succinyl-CoA synthetase (SCS) is a mitochondrial matrix enzyme that acts as a heterodimer, being composed of an invariant alpha subunit and a substrate-specific beta subunit. The protein encoded by this gene is an ATP-specific SCS beta subunit that dimerizes with the SCS alpha subunit to form SCS-A, an essential component of the tricarboxylic acid cycle. SCS-A hydrolyzes ATP to convert succinate to succinyl-CoA. Defects in this gene are a cause of myopathic mitochondrial DNA depletion syndrome. A pseudogene of this gene has been found on chromosome 6. [provided by RefSeq, Jul 2008]".
- SUCLA2 entrezgene "8803".
- SUCLA2 wikiPageExternalLink br.fcgi?book=gene&part=sucla2-def.
- SUCLA2 wikiPageID "15066331".
- SUCLA2 wikiPageLength "13908".
- SUCLA2 wikiPageOutDegree "52".
- SUCLA2 wikiPageRevisionID "704880420".
- SUCLA2 wikiPageWikiLink Acetoacetyl-CoA.
- SUCLA2 wikiPageWikiLink Adenosine_triphosphate.
- SUCLA2 wikiPageWikiLink Alpha-Ketoglutaric_acid.
- SUCLA2 wikiPageWikiLink Amino_acid.
- SUCLA2 wikiPageWikiLink Astrocyte.
- SUCLA2 wikiPageWikiLink Baclofen.
- SUCLA2 wikiPageWikiLink Brain.
- SUCLA2 wikiPageWikiLink Catabolism.
- SUCLA2 wikiPageWikiLink Citric_acid_cycle.
- SUCLA2 wikiPageWikiLink Coenzyme_Q10.
- SUCLA2 wikiPageWikiLink Dystonia.
- SUCLA2 wikiPageWikiLink Enzyme.
- SUCLA2 wikiPageWikiLink Epilepsy.
- SUCLA2 wikiPageWikiLink Exon.
- SUCLA2 wikiPageWikiLink Founder_effect.
- SUCLA2 wikiPageWikiLink Gamma-Aminobutyric_acid.
- SUCLA2 wikiPageWikiLink Gene.
- SUCLA2 wikiPageWikiLink Heart.
- SUCLA2 wikiPageWikiLink Heme.
- SUCLA2 wikiPageWikiLink Hydrolysis.
- SUCLA2 wikiPageWikiLink Hyperkinesia.
- SUCLA2 wikiPageWikiLink Hypotonia.
- SUCLA2 wikiPageWikiLink Ischemia.
- SUCLA2 wikiPageWikiLink Ketone_bodies.
- SUCLA2 wikiPageWikiLink Leigh_disease.
- SUCLA2 wikiPageWikiLink Microglia.
- SUCLA2 wikiPageWikiLink Missense_mutation.
- SUCLA2 wikiPageWikiLink Mitochondrial_DNA_depletion_syndrome.
- SUCLA2 wikiPageWikiLink Mitochondrial_matrix.
- SUCLA2 wikiPageWikiLink Muscle_atrophy.
- SUCLA2 wikiPageWikiLink Myopathy.
- SUCLA2 wikiPageWikiLink Neuron.
- SUCLA2 wikiPageWikiLink Oligodendrocyte.
- SUCLA2 wikiPageWikiLink Protein_dimer.
- SUCLA2 wikiPageWikiLink Protein_subunit.
- SUCLA2 wikiPageWikiLink Pseudogene.
- SUCLA2 wikiPageWikiLink SUCLG1.
- SUCLA2 wikiPageWikiLink SUCLG2.
- SUCLA2 wikiPageWikiLink Scoliosis.
- SUCLA2 wikiPageWikiLink Skeletal_muscle.
- SUCLA2 wikiPageWikiLink Substrate-level_phosphorylation.
- SUCLA2 wikiPageWikiLink Substrate_(chemistry).
- SUCLA2 wikiPageWikiLink Succinic_acid.
- SUCLA2 wikiPageWikiLink Succinyl-CoA.
- SUCLA2 wikiPageWikiLink Succinyl_coenzyme_A_synthetase.
- SUCLA2 wikiPageWikiLinkText "SUCLA2".
- SUCLA2 wikiPageUsesTemplate Template:Cite_journal.
- SUCLA2 wikiPageUsesTemplate Template:PBB.
- SUCLA2 wikiPageUsesTemplate Template:Refbegin.
- SUCLA2 wikiPageUsesTemplate Template:Refend.
- SUCLA2 wikiPageUsesTemplate Template:Reflist.
- SUCLA2 hypernym Enzyme.
- SUCLA2 type Biomolecule.
- SUCLA2 type Protein.
- SUCLA2 type Thing.
- SUCLA2 type Q206229.
- SUCLA2 type Q8054.
- SUCLA2 comment "Succinyl-CoA ligase [ADP-forming] subunit beta, mitochondrial (SUCLA2), also known as ADP-forming succinyl-CoA synthetase (SCS-A), is an enzyme that in humans is encoded by the SUCLA2 gene on chromosome 13.Succinyl-CoA synthetase (SCS) is a mitochondrial matrix enzyme that acts as a heterodimer, being composed of an invariant alpha subunit and a substrate-specific beta subunit.".
- SUCLA2 label "SUCLA2".
- SUCLA2 sameAs Q18033409.
- SUCLA2 sameAs m.03hgcx5.
- SUCLA2 sameAs Q18033409.
- SUCLA2 wasDerivedFrom SUCLA2?oldid=704880420.
- SUCLA2 isPrimaryTopicOf SUCLA2.