Matches in DBpedia 2016-04 for { <http://dbpedia.org/resource/Paroxysmal_nocturnal_hemoglobinuria> ?p ?o }
- Paroxysmal_nocturnal_hemoglobinuria abstract "Paroxysmal nocturnal hemoglobinuria or paroxysmal nocturnal haemoglobinuria (PNH), previously Marchiafava–Micheli syndrome, is a rare, acquired, life-threatening disease of the blood characterized by destruction of red blood cells by the complement system, a part of the body's intrinsic immune system. This destructive process is a result of a defect in the formation of surface proteins on the red blood cell, which normally function to inhibit such immune reactions. Since the complement cascade attacks the red blood cells throughout the circulatory system, the hemolysis is considered an intravascular hemolytic anemia. Other key features of the disease, notably the high incidence of thrombosis, are not totally understood.PNH is the only hemolytic anemia caused by an acquired (rather than inherited) intrinsic defect in the cell membrane (deficiency of glycophosphatidylinositol leading to absence of protective proteins on the membrane). It may develop on its own (\"primary PNH\") or in the context of other bone marrow disorders such as aplastic anemia (\"secondary PNH\"). Only a minority (26%) have the telltale red urine in the morning that originally gave the condition its name.Allogeneic bone marrow transplantation is the only curative therapy, but has significant rates of both mortality and ongoing morbidity. The monoclonal antibody eculizumab is effective at reducing the need for blood transfusions and improving quality of life. It, however, does not appear to change the risk of death or blood clots and has an extremely high price, with a single year of treatment costing at least $440,000.".
- Paroxysmal_nocturnal_hemoglobinuria icd10 "D59.5".
- Paroxysmal_nocturnal_hemoglobinuria icd9 "283.2".
- Paroxysmal_nocturnal_hemoglobinuria meshId "D006457".
- Paroxysmal_nocturnal_hemoglobinuria omim "300818".
- Paroxysmal_nocturnal_hemoglobinuria wikiPageExternalLink www.aamds.org.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageExternalLink www.pnh-alliance.org.uk.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageExternalLink www.pnhfoundation.org.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageExternalLink www.pnhinterestgroup.org.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageID "513180".
- Paroxysmal_nocturnal_hemoglobinuria wikiPageLength "18926".
- Paroxysmal_nocturnal_hemoglobinuria wikiPageOutDegree "95".
- Paroxysmal_nocturnal_hemoglobinuria wikiPageRevisionID "702288543".
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Abdominal_pain.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Acute_myeloid_leukemia.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Allotransplantation.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink American_and_British_English_spelling_differences.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Anemia.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Antibody.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Aplastic_anemia.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Bilirubin.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Blood_test.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Bone_marrow.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Budd–Chiari_syndrome.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink C3-convertase.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink CD59.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Category:Acquired_hemolytic_anemia.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Category:Rare_diseases.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Category:Vascular-related_cutaneous_conditions.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Cell_membrane.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Cerebral_venous_sinus_thrombosis.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Complement_component_9.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Complement_membrane_attack_complex.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Complement_system.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Coombs_test.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Decay-accelerating_factor.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Deep_vein_thrombosis.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Dysphagia.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Dyspnea.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Eculizumab.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Erectile_dysfunction.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Esophageal_spasm.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Flow_cytometry.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Fluorescein-labeled_proaerolysin.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Germany.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Glucocorticoid.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Glycophosphatidylinositol.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Greifswald.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Ham_test.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Haptoglobin.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Heart.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Heart_failure.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Hematopoietic_stem_cell.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Hemoglobin.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Hemoglobinuria.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Hemolysis.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Hemolytic_anemia.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Hemosiderin.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Hepatic_portal_vein.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Hepatic_vein.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Hypoventilation.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Inferior_mesenteric_vein.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Innate_immune_system.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Iron_deficiency.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Lactate_dehydrogenase.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Leukemia.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Mesenteric_ischemia.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Monoclonal_antibody.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Myelodysplastic_syndrome.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Nitric_oxide.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Odynophagia.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Opsonin.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink PIGA.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Palpitations.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Platelet.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Portal_vein_thrombosis.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Prednisolone.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Pulmonary_embolism.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Pulmonary_hypertension.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Red_blood_cell.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Reticulocyte.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Sildenafil.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Smooth_muscle_tissue.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Stroke.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Superior_mesenteric_vein.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Thrombosis.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink Warfarin.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink White_blood_cell.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink X-inactivation.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink X_chromosome.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink File:Cd59.png.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLink File:Protein_CD55_PDB_1h03.png.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLinkText "Paroxysmal nocturnal hemoglobinuria".
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLinkText "Strübing-Marchiafava-Micheli syndrome".
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLinkText "paroxysmal hemoglobinuria".
- Paroxysmal_nocturnal_hemoglobinuria wikiPageWikiLinkText "paroxysmal nocturnal hemoglobinuria".
- Paroxysmal_nocturnal_hemoglobinuria diseasesdb "9688".
- Paroxysmal_nocturnal_hemoglobinuria emedicinesubj "article".
- Paroxysmal_nocturnal_hemoglobinuria emedicinetopic "207468".
- Paroxysmal_nocturnal_hemoglobinuria icd "283.2".