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- Lymphangioleiomyomatosis abstract "Lymphangioleiomyomatosis (LAM) is a rare, progressive, systemic disease that typically results in cystic lung destruction and predominantly affects women, especially during child bearing years. It occurs in more than 30% of women with tuberous sclerosis complex (TSC-LAM), a heritable syndrome that is associated with seizures, cognitive impairment and benign tumors in multiple tissues. Most LAM patients who present for medical evaluation have the sporadic form of the disease (S-LAM), however, which is not associated with other manifestations of tuberous sclerosis complex. Mild cystic changes consistent with LAM have been described in 10-15% of men with TSC, but symptomatic LAM in males is extremely rare. Sporadic LAM occurs exclusively in women, with one published exception to date. Both TSC-LAM and S-LAM are associated with mutations in tuberous sclerosis genes. Lung destruction in LAM is a consequence of diffuse infiltration by neoplastic smooth muscle-like cells, which invade all lung structures including the lymphatics, airway walls, blood vessels, and interstitial spaces. The consequence of obstruction of the vessels and airways include chylous fluid accumulations, hemoptysis, airflow obstruction and pneumothorax. The typical disease course is characterized by progressive dyspnea on exertion, punctuated by recurrent pneumothoraces and, in some patients, chylous pleural effusions or ascites. Modern estimates for median survival in LAM have varied from 10 to 30 years, based on whether hospital based or population based cohorts are studied. Most patients have dyspnea on exertion with daily activities by 10 years after symptom onset and many will require supplemental oxygen over that interval. An FDA approved drug for treatment of LAM, sirolimus, is now available for stabilization of lung function decline. Lung transplant remains the option of last resort for patients with advanced disease.".
- Lymphangioleiomyomatosis icd10 "J84.81".
- Lymphangioleiomyomatosis icd9 "516.4".
- Lymphangioleiomyomatosis icdo "9174/1".
- Lymphangioleiomyomatosis meshId "D018192".
- Lymphangioleiomyomatosis omim "606690".
- Lymphangioleiomyomatosis thumbnail Lymphangioleiomyomatosis.jpg?width=300.
- Lymphangioleiomyomatosis wikiPageExternalLink lam-israel.org.
- Lymphangioleiomyomatosis wikiPageExternalLink lammexico.org.
- Lymphangioleiomyomatosis wikiPageExternalLink www.J-LAM.net.
- Lymphangioleiomyomatosis wikiPageExternalLink www.aelam.org.
- Lymphangioleiomyomatosis wikiPageExternalLink index.php.
- Lymphangioleiomyomatosis wikiPageExternalLink www.francelam.org.
- Lymphangioleiomyomatosis wikiPageExternalLink www.lam-info.de.
- Lymphangioleiomyomatosis wikiPageExternalLink www.lam-italia.org.
- Lymphangioleiomyomatosis wikiPageExternalLink www.lam-nederland.nl.
- Lymphangioleiomyomatosis wikiPageExternalLink www.lam.org.nz.
- Lymphangioleiomyomatosis wikiPageExternalLink www.lamacademy.org.
- Lymphangioleiomyomatosis wikiPageExternalLink www.lamaction.org.
- Lymphangioleiomyomatosis wikiPageExternalLink www.lamaustralia.org.au.
- Lymphangioleiomyomatosis wikiPageExternalLink www.lamaustria.com.
- Lymphangioleiomyomatosis wikiPageExternalLink www.lamchina.org.
- Lymphangioleiomyomatosis wikiPageExternalLink www.lamromania.ro.
- Lymphangioleiomyomatosis wikiPageExternalLink www.thelamfoundation.org.
- Lymphangioleiomyomatosis wikiPageExternalLink lymphangioleiomyomatosis-lam.pdf.
- Lymphangioleiomyomatosis wikiPageID "1721174".
- Lymphangioleiomyomatosis wikiPageLength "100891".
- Lymphangioleiomyomatosis wikiPageOutDegree "21".
- Lymphangioleiomyomatosis wikiPageRevisionID "706706874".
- Lymphangioleiomyomatosis wikiPageWikiLink Angiomyolipoma.
- Lymphangioleiomyomatosis wikiPageWikiLink Category:Lung_disorders.
- Lymphangioleiomyomatosis wikiPageWikiLink Category:Lymphatic_vessel_diseases.
- Lymphangioleiomyomatosis wikiPageWikiLink Category:Rare_diseases.
- Lymphangioleiomyomatosis wikiPageWikiLink Chyle.
- Lymphangioleiomyomatosis wikiPageWikiLink Chylopericaridium.
- Lymphangioleiomyomatosis wikiPageWikiLink Chyloptysis.
- Lymphangioleiomyomatosis wikiPageWikiLink Chylothorax.
- Lymphangioleiomyomatosis wikiPageWikiLink Chyluria.
- Lymphangioleiomyomatosis wikiPageWikiLink File:Diagnostic_Algorithm_for_Lymphangioleiomyomatosis.jpg.
- Lymphangioleiomyomatosis wikiPageWikiLink Hemoptysis.
- Lymphangioleiomyomatosis wikiPageWikiLink House_(TV_series).
- Lymphangioleiomyomatosis wikiPageWikiLink Lucky_Thirteen_(House).
- Lymphangioleiomyomatosis wikiPageWikiLink National_Center_for_Advancing_Translational_Sciences.
- Lymphangioleiomyomatosis wikiPageWikiLink National_Institutes_of_Health.
- Lymphangioleiomyomatosis wikiPageWikiLink Perivascular_epithelioid_cell_tumour.
- Lymphangioleiomyomatosis wikiPageWikiLink Rare_Diseases_Clinical_Research_Network.
- Lymphangioleiomyomatosis wikiPageWikiLink Sirolimus.
- Lymphangioleiomyomatosis wikiPageWikiLink Sjxc3xb6grens_syndrome.
- Lymphangioleiomyomatosis wikiPageWikiLink File:Lymphangioleiomyomatose_CT.jpg.
- Lymphangioleiomyomatosis wikiPageWikiLink File:Lymphangioleiomyomatosis_-_low_mag.jpg.
- Lymphangioleiomyomatosis wikiPageWikiLinkText "LAM Action".
- Lymphangioleiomyomatosis wikiPageWikiLinkText "Lymphangioleiomyomatosis".
- Lymphangioleiomyomatosis wikiPageWikiLinkText "lymphangioleiomyomatosis".
- Lymphangioleiomyomatosis caption "Figure A shows the location of the lungs and airways in the body. The inset image shows a cross-section of a healthy lung. Figure B shows a view of the lungs with LAM and a collapsed lung . The inset image shows a cross-section of a lung with LAM.".
- Lymphangioleiomyomatosis diseasesdb "30755".
- Lymphangioleiomyomatosis emedicinesubj "med".
- Lymphangioleiomyomatosis emedicinetopic "1348".
- Lymphangioleiomyomatosis icd "516.4".
- Lymphangioleiomyomatosis icd "J84.81".
- Lymphangioleiomyomatosis icdo "9174".
- Lymphangioleiomyomatosis meshid "D018192".
- Lymphangioleiomyomatosis name "Lymphangioleiomyomatosis".
- Lymphangioleiomyomatosis omim "606690".
- Lymphangioleiomyomatosis wikiPageUsesTemplate Template:EMedicine2.
- Lymphangioleiomyomatosis wikiPageUsesTemplate Template:Infobox_disease.
- Lymphangioleiomyomatosis wikiPageUsesTemplate Template:Reflist.
- Lymphangioleiomyomatosis wikiPageUsesTemplate Template:Vascular_tumors.
- Lymphangioleiomyomatosis subject Category:Lung_disorders.
- Lymphangioleiomyomatosis subject Category:Lymphatic_vessel_diseases.
- Lymphangioleiomyomatosis subject Category:Rare_diseases.
- Lymphangioleiomyomatosis hypernym Disease.
- Lymphangioleiomyomatosis type Disease.
- Lymphangioleiomyomatosis type Disorder.
- Lymphangioleiomyomatosis type Thing.
- Lymphangioleiomyomatosis type Q12136.
- Lymphangioleiomyomatosis comment "Lymphangioleiomyomatosis (LAM) is a rare, progressive, systemic disease that typically results in cystic lung destruction and predominantly affects women, especially during child bearing years. It occurs in more than 30% of women with tuberous sclerosis complex (TSC-LAM), a heritable syndrome that is associated with seizures, cognitive impairment and benign tumors in multiple tissues.".
- Lymphangioleiomyomatosis label "Lymphangioleiomyomatosis".
- Lymphangioleiomyomatosis sameAs Q1878759.
- Lymphangioleiomyomatosis sameAs Lymphangioleiomyomatose.
- Lymphangioleiomyomatosis sameAs Lymphangioléiomyomatose.
- Lymphangioleiomyomatosis sameAs Linfangioleiomiomatosi.
- Lymphangioleiomyomatosis sameAs リンパ脈管筋腫症.
- Lymphangioleiomyomatosis sameAs Lymfangioleiomyomatose.
- Lymphangioleiomyomatosis sameAs Limfangioleiomiomatoza.
- Lymphangioleiomyomatosis sameAs Linfangioleiomiomatose.
- Lymphangioleiomyomatosis sameAs m.05r1dv.
- Lymphangioleiomyomatosis sameAs Лимфангиолейомиоматоз.
- Lymphangioleiomyomatosis sameAs Lenfanjiyoleyomiyomatozis.
- Lymphangioleiomyomatosis sameAs سیالہ_وعائی_ہمعضلومہ.
- Lymphangioleiomyomatosis sameAs Q1878759.
- Lymphangioleiomyomatosis wasDerivedFrom Lymphangioleiomyomatosis?oldid=706706874.
- Lymphangioleiomyomatosis depiction Lymphangioleiomyomatosis.jpg.
- Lymphangioleiomyomatosis isPrimaryTopicOf Lymphangioleiomyomatosis.
- Lymphangioleiomyomatosis name "Lymphangioleiomyomatosis".