Matches in DBpedia 2016-04 for { <http://dbpedia.org/resource/Isolated_primary_immunoglobulin_M_deficiency> ?p ?o }
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- Isolated_primary_immunoglobulin_M_deficiency abstract "Isolated primary immunoglobulin M deficiency (or selective IgM immunodeficiency (SIgMD)) is a poorly defined dysgammaglobulinemia characterized by decreased levels of IgM while levels of other immunoglobulins are normal. The immunodeficiency has been associated with some clinical disorders including recurrent infections, atopy, Bloom's syndrome, celiac disease, systemic lupus erythematosus and malignancy, but, surprisingly, SIgMD seems to also occur in asymptomatic individuals. High incidences of recurrent upper respiratory tract infections (77%), asthma (47%) and allergic rhinitis (36%) have also been reported. SIgMD seems to be a particularly rare antibody deficiency with a reported prevalence between 0.03% (general population) and 0.1% (hospitalized patients).The etiology of selective IgM deficiency remains unclear, although various mechanisms have been proposed, such as an increase in regulatory T cell functions, defective T helper cell functions and impaired terminal differentiation of B lymphocytes into IgM-secreting cells among others. It is however puzzling that class switching seems to happen normally (serum levels of other antibodies are normal), while dysfunctioning of IgM synthesis is expected to occur together with abnormalities in other immunoglobulins. Notwithstanding a clear pathogenesis and commonly accepted definition, a cutoff for SIgMD could be the lower limit of the serum IgM reference range, such as 43 mg/dL in adults or even 20 mg/dL.".
- Isolated_primary_immunoglobulin_M_deficiency thumbnail IgM_scheme.svg?width=300.
- Isolated_primary_immunoglobulin_M_deficiency wikiPageID "18386524".
- Isolated_primary_immunoglobulin_M_deficiency wikiPageLength "3668".
- Isolated_primary_immunoglobulin_M_deficiency wikiPageOutDegree "20".
- Isolated_primary_immunoglobulin_M_deficiency wikiPageRevisionID "668964894".
- Isolated_primary_immunoglobulin_M_deficiency wikiPageWikiLink Allergic_rhinitis.
- Isolated_primary_immunoglobulin_M_deficiency wikiPageWikiLink Antibody.
- Isolated_primary_immunoglobulin_M_deficiency wikiPageWikiLink Asthma.
- Isolated_primary_immunoglobulin_M_deficiency wikiPageWikiLink Atopy.
- Isolated_primary_immunoglobulin_M_deficiency wikiPageWikiLink B_cell.
- Isolated_primary_immunoglobulin_M_deficiency wikiPageWikiLink Bloom_syndrome.
- Isolated_primary_immunoglobulin_M_deficiency wikiPageWikiLink Category:Noninfectious_immunodeficiency-related_cutaneous_conditions.
- Isolated_primary_immunoglobulin_M_deficiency wikiPageWikiLink Category:Predominantly_antibody_deficiencies.
- Isolated_primary_immunoglobulin_M_deficiency wikiPageWikiLink Coeliac_disease.
- Isolated_primary_immunoglobulin_M_deficiency wikiPageWikiLink Dysgammaglobulinemia.
- Isolated_primary_immunoglobulin_M_deficiency wikiPageWikiLink Immunodeficiency_with_hyperimmunoglobulin_M.
- Isolated_primary_immunoglobulin_M_deficiency wikiPageWikiLink Immunoglobulin_M.
- Isolated_primary_immunoglobulin_M_deficiency wikiPageWikiLink Immunoglobulin_class_switching.
- Isolated_primary_immunoglobulin_M_deficiency wikiPageWikiLink List_of_cutaneous_conditions.
- Isolated_primary_immunoglobulin_M_deficiency wikiPageWikiLink Regulatory_T_cell.
- Isolated_primary_immunoglobulin_M_deficiency wikiPageWikiLink Systemic_lupus_erythematosus.
- Isolated_primary_immunoglobulin_M_deficiency wikiPageWikiLink T_helper_cell.
- Isolated_primary_immunoglobulin_M_deficiency wikiPageWikiLinkText "Isolated primary immunoglobulin M deficiency".
- Isolated_primary_immunoglobulin_M_deficiency caption Immunoglobulin_M.
- Isolated_primary_immunoglobulin_M_deficiency emedicinesubj "med".
- Isolated_primary_immunoglobulin_M_deficiency emedicinetopic "3436".
- Isolated_primary_immunoglobulin_M_deficiency icd "279.02".
- Isolated_primary_immunoglobulin_M_deficiency icd "D80.4".
- Isolated_primary_immunoglobulin_M_deficiency name "Isolated primary immunoglobulin M deficiency".
- Isolated_primary_immunoglobulin_M_deficiency wikiPageUsesTemplate Template:Immune_disorders.
- Isolated_primary_immunoglobulin_M_deficiency wikiPageUsesTemplate Template:Infobox_Disease.
- Isolated_primary_immunoglobulin_M_deficiency wikiPageUsesTemplate Template:Reflist.
- Isolated_primary_immunoglobulin_M_deficiency subject Category:Noninfectious_immunodeficiency-related_cutaneous_conditions.
- Isolated_primary_immunoglobulin_M_deficiency subject Category:Predominantly_antibody_deficiencies.
- Isolated_primary_immunoglobulin_M_deficiency comment "Isolated primary immunoglobulin M deficiency (or selective IgM immunodeficiency (SIgMD)) is a poorly defined dysgammaglobulinemia characterized by decreased levels of IgM while levels of other immunoglobulins are normal. The immunodeficiency has been associated with some clinical disorders including recurrent infections, atopy, Bloom's syndrome, celiac disease, systemic lupus erythematosus and malignancy, but, surprisingly, SIgMD seems to also occur in asymptomatic individuals.".
- Isolated_primary_immunoglobulin_M_deficiency label "Isolated primary immunoglobulin M deficiency".
- Isolated_primary_immunoglobulin_M_deficiency sameAs Q6085903.
- Isolated_primary_immunoglobulin_M_deficiency sameAs m.04f3jgr.
- Isolated_primary_immunoglobulin_M_deficiency sameAs Недостаточность_иммуноглобулина_M.
- Isolated_primary_immunoglobulin_M_deficiency sameAs Q6085903.
- Isolated_primary_immunoglobulin_M_deficiency wasDerivedFrom Isolated_primary_immunoglobulin_M_deficiency?oldid=668964894.
- Isolated_primary_immunoglobulin_M_deficiency depiction IgM_scheme.svg.
- Isolated_primary_immunoglobulin_M_deficiency isPrimaryTopicOf Isolated_primary_immunoglobulin_M_deficiency.