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- Hereditary_pyropoikilocytosis abstract "Hereditary pyropoikilocytosis (HPP) is an autosomal recessive form of hemolytic anemia characterized by an abnormal sensitivity of red blood cells to heat and erythrocyte morphology similar to that seen in thermal burns. Patients with HPP tend to experience severe haemolysis and anaemia in infancy that gradually improves, evolving toward typical elliptocytosis later in life. However, the hemolysis can lead to rapid sequestration and destruction of red cells. Splenectomy is curative when this occurs.HPP has been associated with a defect of the erythrocyte membrane protein spectrin and with spectrin deficiency.It was characterized in 1975.It is considered a severe form of hereditary elliptocytosis.".
- Hereditary_pyropoikilocytosis omim "266140".
- Hereditary_pyropoikilocytosis wikiPageID "3725759".
- Hereditary_pyropoikilocytosis wikiPageLength "2760".
- Hereditary_pyropoikilocytosis wikiPageOutDegree "15".
- Hereditary_pyropoikilocytosis wikiPageRevisionID "641910933".
- Hereditary_pyropoikilocytosis wikiPageWikiLink Anemia.
- Hereditary_pyropoikilocytosis wikiPageWikiLink Category:Autosomal_recessive_disorders.
- Hereditary_pyropoikilocytosis wikiPageWikiLink Category:Cytoskeletal_defects.
- Hereditary_pyropoikilocytosis wikiPageWikiLink Category:Red_blood_cell_disorders.
- Hereditary_pyropoikilocytosis wikiPageWikiLink Dominance_(genetics).
- Hereditary_pyropoikilocytosis wikiPageWikiLink Hemolysis.
- Hereditary_pyropoikilocytosis wikiPageWikiLink Hemolytic_anemia.
- Hereditary_pyropoikilocytosis wikiPageWikiLink Hereditary_elliptocytosis.
- Hereditary_pyropoikilocytosis wikiPageWikiLink List_of_hematologic_conditions.
- Hereditary_pyropoikilocytosis wikiPageWikiLink Poikilocytosis.
- Hereditary_pyropoikilocytosis wikiPageWikiLink Red_blood_cell.
- Hereditary_pyropoikilocytosis wikiPageWikiLink Spectrin.
- Hereditary_pyropoikilocytosis wikiPageWikiLink Spectrin_deficiency.
- Hereditary_pyropoikilocytosis wikiPageWikiLinkText "Hereditary pyropoikilocytosis".
- Hereditary_pyropoikilocytosis wikiPageWikiLinkText "hereditary pyropoikilocytosis".
- Hereditary_pyropoikilocytosis name "Hereditary pyropoikilocytosis".
- Hereditary_pyropoikilocytosis omim "266140".
- Hereditary_pyropoikilocytosis wikiPageUsesTemplate Template:Blood-disease-stub.
- Hereditary_pyropoikilocytosis wikiPageUsesTemplate Template:Cytoskeletal_defects.
- Hereditary_pyropoikilocytosis wikiPageUsesTemplate Template:Infobox_disease.
- Hereditary_pyropoikilocytosis wikiPageUsesTemplate Template:Reflist.
- Hereditary_pyropoikilocytosis subject Category:Autosomal_recessive_disorders.
- Hereditary_pyropoikilocytosis subject Category:Cytoskeletal_defects.
- Hereditary_pyropoikilocytosis subject Category:Red_blood_cell_disorders.
- Hereditary_pyropoikilocytosis hypernym Form.
- Hereditary_pyropoikilocytosis type Disease.
- Hereditary_pyropoikilocytosis type Defect.
- Hereditary_pyropoikilocytosis type Disorder.
- Hereditary_pyropoikilocytosis type Thing.
- Hereditary_pyropoikilocytosis type Q12136.
- Hereditary_pyropoikilocytosis comment "Hereditary pyropoikilocytosis (HPP) is an autosomal recessive form of hemolytic anemia characterized by an abnormal sensitivity of red blood cells to heat and erythrocyte morphology similar to that seen in thermal burns. Patients with HPP tend to experience severe haemolysis and anaemia in infancy that gradually improves, evolving toward typical elliptocytosis later in life. However, the hemolysis can lead to rapid sequestration and destruction of red cells.".
- Hereditary_pyropoikilocytosis label "Hereditary pyropoikilocytosis".
- Hereditary_pyropoikilocytosis sameAs Q5737872.
- Hereditary_pyropoikilocytosis sameAs m.09xfwv.
- Hereditary_pyropoikilocytosis sameAs Q5737872.
- Hereditary_pyropoikilocytosis wasDerivedFrom Hereditary_pyropoikilocytosis?oldid=641910933.
- Hereditary_pyropoikilocytosis isPrimaryTopicOf Hereditary_pyropoikilocytosis.
- Hereditary_pyropoikilocytosis name "Hereditary pyropoikilocytosis".