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- Glycogen_debranching_enzyme abstract "A debranching enzyme is a molecule that helps facilitate the breakdown of glycogen, which serves as a store of glucose in the body, through glucosyltransferase and glucosidase activity. Together with phosphorylases, debranching enzymes mobilize glucose reserves from glycogen deposits in the muscles and liver. This constitutes a major source of energy reserves in most organisms. Glycogen breakdown is highly regulated in the body, especially in the liver, by various hormones including insulin and glucagon, to maintain a homeostatic balance of blood-glucose levels. When glycogen breakdown is compromised by mutations in the glycogen debranching enzyme, metabolic diseases such as Glycogen storage disease type III can result.Glucosyltransferase and glucosidase are performed by a single enzyme in mammals, yeast, and some bacteria, but by two distinct enzymes in E. coli and other bacteria, complicating nomenclature. Proteins that catalyze both functions are referred to as glycogen debranching enzymes (GDEs). When glucosyltransferase and glucosidase are catalyzed by distinct enzymes, \"glycogen debranching enzyme\" usually refers to the glucosidase enzyme. In some literature, an enzyme capable only of glucosidase is referred to as a \"debranching enzyme\".".
- Glycogen_debranching_enzyme entrezgene "178".
- Glycogen_debranching_enzyme thumbnail Glycogen_Debranching_Enzyme.png?width=300.
- Glycogen_debranching_enzyme wikiPageExternalLink br.fcgi?book=gene&part=gsd3.
- Glycogen_debranching_enzyme wikiPageExternalLink 232400,610860,232400,610860.
- Glycogen_debranching_enzyme wikiPageID "2940689".
- Glycogen_debranching_enzyme wikiPageLength "20966".
- Glycogen_debranching_enzyme wikiPageOutDegree "47".
- Glycogen_debranching_enzyme wikiPageRevisionID "699072089".
- Glycogen_debranching_enzyme wikiPageWikiLink 4-alpha-glucanotransferase.
- Glycogen_debranching_enzyme wikiPageWikiLink Active_site.
- Glycogen_debranching_enzyme wikiPageWikiLink Amino_acid.
- Glycogen_debranching_enzyme wikiPageWikiLink Archaea.
- Glycogen_debranching_enzyme wikiPageWikiLink Cardiomyopathy.
- Glycogen_debranching_enzyme wikiPageWikiLink Category:EC_2.4.1.
- Glycogen_debranching_enzyme wikiPageWikiLink Category:EC_3.2.1.
- Glycogen_debranching_enzyme wikiPageWikiLink Enzyme.
- Glycogen_debranching_enzyme wikiPageWikiLink Escherichia_coli.
- Glycogen_debranching_enzyme wikiPageWikiLink Eukaryote.
- Glycogen_debranching_enzyme wikiPageWikiLink Exon.
- Glycogen_debranching_enzyme wikiPageWikiLink Gene_expression.
- Glycogen_debranching_enzyme wikiPageWikiLink Glucagon.
- Glycogen_debranching_enzyme wikiPageWikiLink Glucose.
- Glycogen_debranching_enzyme wikiPageWikiLink Glucosidases.
- Glycogen_debranching_enzyme wikiPageWikiLink Glucosyltransferase.
- Glycogen_debranching_enzyme wikiPageWikiLink Glycogen.
- Glycogen_debranching_enzyme wikiPageWikiLink Glycogen_storage_disease_type_III.
- Glycogen_debranching_enzyme wikiPageWikiLink Glycogenolysis.
- Glycogen_debranching_enzyme wikiPageWikiLink Hepatomegaly.
- Glycogen_debranching_enzyme wikiPageWikiLink Hydrolysis.
- Glycogen_debranching_enzyme wikiPageWikiLink Hypertrophy.
- Glycogen_debranching_enzyme wikiPageWikiLink Hypoglycemia.
- Glycogen_debranching_enzyme wikiPageWikiLink Insulin.
- Glycogen_debranching_enzyme wikiPageWikiLink Isoamylase.
- Glycogen_debranching_enzyme wikiPageWikiLink Liver.
- Glycogen_debranching_enzyme wikiPageWikiLink Maltotetraose.
- Glycogen_debranching_enzyme wikiPageWikiLink Mutation.
- Glycogen_debranching_enzyme wikiPageWikiLink Myopathy.
- Glycogen_debranching_enzyme wikiPageWikiLink Nucleophile.
- Glycogen_debranching_enzyme wikiPageWikiLink Oxocarbenium.
- Glycogen_debranching_enzyme wikiPageWikiLink Phosphorylase.
- Glycogen_debranching_enzyme wikiPageWikiLink Protein_isoform.
- Glycogen_debranching_enzyme wikiPageWikiLink Residue_(chemistry).
- Glycogen_debranching_enzyme wikiPageWikiLink Sulfolobus_solfataricus.
- Glycogen_debranching_enzyme wikiPageWikiLink Uric_acid.
- Glycogen_debranching_enzyme wikiPageWikiLink Yeast.
- Glycogen_debranching_enzyme wikiPageWikiLink File:Glycogen_Debranching_Enzyme.png.
- Glycogen_debranching_enzyme wikiPageWikiLink File:Glycosidase_mechanism.png.
- Glycogen_debranching_enzyme wikiPageWikiLink File:Hypothesized_substraight_binding_location.png.
- Glycogen_debranching_enzyme wikiPageWikiLinkText "Debranching enzyme".
- Glycogen_debranching_enzyme wikiPageWikiLinkText "Glycogen debranching enzyme".
- Glycogen_debranching_enzyme wikiPageWikiLinkText "debranching enzyme".
- Glycogen_debranching_enzyme wikiPageWikiLinkText "glycogen debranching enzyme".
- Glycogen_debranching_enzyme wikiPageWikiLinkText "α1-6 glucosidase".
- Glycogen_debranching_enzyme casNumber "9012".
- Glycogen_debranching_enzyme casNumber "9032-09-01".
- Glycogen_debranching_enzyme colwidth "35".
- Glycogen_debranching_enzyme ecNumber "2.4".
- Glycogen_debranching_enzyme ecNumber "3.2".
- Glycogen_debranching_enzyme goCode "4134".
- Glycogen_debranching_enzyme goCode "4135".
- Glycogen_debranching_enzyme iubmbEcNumber "2".
- Glycogen_debranching_enzyme iubmbEcNumber "3".
- Glycogen_debranching_enzyme name "4".
- Glycogen_debranching_enzyme name "amylo-α-1,6-glucosidase".
- Glycogen_debranching_enzyme wikiPageUsesTemplate Template:EC_number.
- Glycogen_debranching_enzyme wikiPageUsesTemplate Template:Enzyme.
- Glycogen_debranching_enzyme wikiPageUsesTemplate Template:Enzymes.
- Glycogen_debranching_enzyme wikiPageUsesTemplate Template:Glycogenesis_and_glycogenolysis_enzymes.
- Glycogen_debranching_enzyme wikiPageUsesTemplate Template:Glycosyltransferases.
- Glycogen_debranching_enzyme wikiPageUsesTemplate Template:Main.
- Glycogen_debranching_enzyme wikiPageUsesTemplate Template:MeSH_name.
- Glycogen_debranching_enzyme wikiPageUsesTemplate Template:PBB.
- Glycogen_debranching_enzyme wikiPageUsesTemplate Template:Portal_bar.
- Glycogen_debranching_enzyme wikiPageUsesTemplate Template:Reflist.
- Glycogen_debranching_enzyme wikiPageUsesTemplate Template:Sugar_hydrolases.
- Glycogen_debranching_enzyme subject Category:EC_2.4.1.
- Glycogen_debranching_enzyme subject Category:EC_3.2.1.
- Glycogen_debranching_enzyme hypernym Molecule.
- Glycogen_debranching_enzyme type Biomolecule.
- Glycogen_debranching_enzyme type ChemicalCompound.
- Glycogen_debranching_enzyme type Protein.
- Glycogen_debranching_enzyme type Thing.
- Glycogen_debranching_enzyme type Q206229.
- Glycogen_debranching_enzyme type Q8054.
- Glycogen_debranching_enzyme comment "A debranching enzyme is a molecule that helps facilitate the breakdown of glycogen, which serves as a store of glucose in the body, through glucosyltransferase and glucosidase activity. Together with phosphorylases, debranching enzymes mobilize glucose reserves from glycogen deposits in the muscles and liver. This constitutes a major source of energy reserves in most organisms.".
- Glycogen_debranching_enzyme label "Glycogen debranching enzyme".
- Glycogen_debranching_enzyme sameAs Q17815968.
- Glycogen_debranching_enzyme sameAs Glykogen-Debranching-Enzym.
- Glycogen_debranching_enzyme sameAs Enzima_desramificadora_del_glucógeno.
- Glycogen_debranching_enzyme sameAs Enzyme_de_débranchement_du_glycogène.
- Glycogen_debranching_enzyme sameAs m.08f1vm.
- Glycogen_debranching_enzyme sameAs Q17815968.
- Glycogen_debranching_enzyme wasDerivedFrom Glycogen_debranching_enzyme?oldid=699072089.
- Glycogen_debranching_enzyme depiction Glycogen_Debranching_Enzyme.png.
- Glycogen_debranching_enzyme isPrimaryTopicOf Glycogen_debranching_enzyme.