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- Glutaryl-CoA_dehydrogenase abstract "Glutaryl-CoA dehydrogenase (GCDH) is an enzyme encoded by the GCDH gene on chromosome 19. The protein belongs to the acyl-CoA dehydrogenase family (ACD). It catalyzes the oxidative decarboxylation of glutaryl-CoA to crotonyl-CoA and carbon dioxide in the degradative pathway of L-lysine, L-hydroxylysine, and L-tryptophan metabolism. It uses electron transfer flavoprotein as its electron acceptor. The enzyme exists in the mitochondrial matrix as a homotetramer of 45-kD subunits. Mutations in this gene result in the metabolic disorder glutaric aciduria type 1, which is also known as glutaric acidemia type I. Alternative splicing of this gene results in multiple transcript variants.".
- Glutaryl-CoA_dehydrogenase entrezgene "2639".
- Glutaryl-CoA_dehydrogenase wikiPageID "9754681".
- Glutaryl-CoA_dehydrogenase wikiPageLength "6184".
- Glutaryl-CoA_dehydrogenase wikiPageOutDegree "51".
- Glutaryl-CoA_dehydrogenase wikiPageRevisionID "697556883".
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Active_site.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Acyl_CoA_dehydrogenase.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Alpha-Hydroxyglutaric_acid.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Alpha_helix.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Ataxia.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Atomic_mass_unit.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Beta_sheet.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink C-terminus.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Carbon.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Carbon_dioxide.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Category:EC_1.3.8.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Choreoathetosis.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Chromosome.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Crotonyl-CoA.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Dimer_(chemistry).
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Dyskinesia.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Dystonia.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Electron-transferring_flavoprotein.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Encephalitis.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Enzyme.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Epileptic_seizure.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Exon.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Flavin_adenine_dinucleotide.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Gene.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Glutaric_acid.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Glutaric_aciduria_type_1.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Glutaryl-CoA.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Homotetramer.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Hydride.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Hydroxylysine.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Ion.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Lysine.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Macrocephaly.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Metabolism.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Metabolite.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Mitochondrial_matrix.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Monomer.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Mutation.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink N-terminus.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Oxidative_decarboxylation.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Peptide.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Properties_of_water.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Protein.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Proton.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink RNA_splicing.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Spasticity.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Substrate_(biology).
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Tetrahedral_symmetry.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Transcription_(genetics).
- Glutaryl-CoA_dehydrogenase wikiPageWikiLink Tryptophan.
- Glutaryl-CoA_dehydrogenase wikiPageWikiLinkText "Glutaryl-CoA dehydrogenase".
- Glutaryl-CoA_dehydrogenase wikiPageWikiLinkText "glutaryl-CoA dehydrogenase".
- Glutaryl-CoA_dehydrogenase wikiPageWikiLinkText "glutaryl-coenzyme A dehydrogenase".
- Glutaryl-CoA_dehydrogenase casNumber "37255".
- Glutaryl-CoA_dehydrogenase ecNumber "1.3".
- Glutaryl-CoA_dehydrogenase name "glutaryl-CoA dehydrogenase".
- Glutaryl-CoA_dehydrogenase wikiPageUsesTemplate Template:Amino_acid_metabolism_enzymes.
- Glutaryl-CoA_dehydrogenase wikiPageUsesTemplate Template:Biochemistry-stub.
- Glutaryl-CoA_dehydrogenase wikiPageUsesTemplate Template:CH-CH_oxidoreductases.
- Glutaryl-CoA_dehydrogenase wikiPageUsesTemplate Template:Enzymes.
- Glutaryl-CoA_dehydrogenase wikiPageUsesTemplate Template:Infobox_enzyme.
- Glutaryl-CoA_dehydrogenase wikiPageUsesTemplate Template:MeshName.
- Glutaryl-CoA_dehydrogenase wikiPageUsesTemplate Template:PBB.
- Glutaryl-CoA_dehydrogenase wikiPageUsesTemplate Template:Portal.
- Glutaryl-CoA_dehydrogenase wikiPageUsesTemplate Template:Reflist.
- Glutaryl-CoA_dehydrogenase subject Category:EC_1.3.8.
- Glutaryl-CoA_dehydrogenase hypernym Enzyme.
- Glutaryl-CoA_dehydrogenase type Biomolecule.
- Glutaryl-CoA_dehydrogenase type Protein.
- Glutaryl-CoA_dehydrogenase type Thing.
- Glutaryl-CoA_dehydrogenase type Q206229.
- Glutaryl-CoA_dehydrogenase type Q8054.
- Glutaryl-CoA_dehydrogenase comment "Glutaryl-CoA dehydrogenase (GCDH) is an enzyme encoded by the GCDH gene on chromosome 19. The protein belongs to the acyl-CoA dehydrogenase family (ACD). It catalyzes the oxidative decarboxylation of glutaryl-CoA to crotonyl-CoA and carbon dioxide in the degradative pathway of L-lysine, L-hydroxylysine, and L-tryptophan metabolism. It uses electron transfer flavoprotein as its electron acceptor. The enzyme exists in the mitochondrial matrix as a homotetramer of 45-kD subunits.".
- Glutaryl-CoA_dehydrogenase label "Glutaryl-CoA dehydrogenase".
- Glutaryl-CoA_dehydrogenase sameAs Q18025598.
- Glutaryl-CoA_dehydrogenase sameAs m.02pr59w.
- Glutaryl-CoA_dehydrogenase sameAs Q18025598.
- Glutaryl-CoA_dehydrogenase wasDerivedFrom Glutaryl-CoA_dehydrogenase?oldid=697556883.
- Glutaryl-CoA_dehydrogenase isPrimaryTopicOf Glutaryl-CoA_dehydrogenase.