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- Fatty-acid_metabolism_disorder abstract "A broad classification for genetic disorders that result from an inability of the body to produce or utilize one enzyme that is required to oxidize fatty acids. The enzyme can be missing or improperly constructed, resulting in it not working. This leaves the body unable to produce energy within the liver and muscles from fatty acid sources.The body's primary source of energy is glucose; however, when all the glucose in the body has been expended, a normal body digests fats. Individuals with a fatty-acid metabolism disorder are unable to metabolize this fat source for energy, halting bodily processes. Most individuals with a fatty-acid metabolism disorder are able to live a normal active life with simple adjustments to diet and medications. If left undiagnosed many complications can arise. When in need of glucose the body of a person with a fatty-acid metabolism disorder will still send fats to the liver. The fats are broken down to fatty acids. The fatty acids are then transported to the target cells but are unable to be broken down, resulting in a build-up of fatty acids in the liver and other internal organs.Fatty-acid metabolism disorders are sometimes classified with the lipid metabolism disorders, but in other contexts they are considered a distinct category.".
- Fatty-acid_metabolism_disorder thumbnail Acyl-CoA2.svg?width=300.
- Fatty-acid_metabolism_disorder wikiPageExternalLink parentpage.htm.
- Fatty-acid_metabolism_disorder wikiPageID "21933440".
- Fatty-acid_metabolism_disorder wikiPageLength "8555".
- Fatty-acid_metabolism_disorder wikiPageOutDegree "20".
- Fatty-acid_metabolism_disorder wikiPageRevisionID "678814116".
- Fatty-acid_metabolism_disorder wikiPageWikiLink Acyl-CoA.
- Fatty-acid_metabolism_disorder wikiPageWikiLink Beta_oxidation.
- Fatty-acid_metabolism_disorder wikiPageWikiLink Carnitine.
- Fatty-acid_metabolism_disorder wikiPageWikiLink Category:Autosomal_recessive_disorders.
- Fatty-acid_metabolism_disorder wikiPageWikiLink Category:Fatty-acid_metabolism_disorders.
- Fatty-acid_metabolism_disorder wikiPageWikiLink Enzyme.
- Fatty-acid_metabolism_disorder wikiPageWikiLink Fatty_acid.
- Fatty-acid_metabolism_disorder wikiPageWikiLink Fatty_acid_metabolism.
- Fatty-acid_metabolism_disorder wikiPageWikiLink File:LCHAD_deficiency.jpg.
- Fatty-acid_metabolism_disorder wikiPageWikiLink Genetic_disorder.
- Fatty-acid_metabolism_disorder wikiPageWikiLink Inborn_error_of_lipid_metabolism.
- Fatty-acid_metabolism_disorder wikiPageWikiLink Long-chain_3-hydroxyacyl-coenzyme_A_dehydrogenase_deficiency.
- Fatty-acid_metabolism_disorder wikiPageWikiLink Medium-chain_acyl-coenzyme_A_dehydrogenase_deficiency.
- Fatty-acid_metabolism_disorder wikiPageWikiLink Mitochondrial_trifunctional_protein_deficiency.
- Fatty-acid_metabolism_disorder wikiPageWikiLink Mitochondrion.
- Fatty-acid_metabolism_disorder wikiPageWikiLink Redox.
- Fatty-acid_metabolism_disorder wikiPageWikiLink Very_long-chain_acyl-coenzyme_A_dehydrogenase_deficiency.
- Fatty-acid_metabolism_disorder wikiPageWikiLink File:Acyl-CoA_from_cytosol_to_the_mitochondrial_matrix.svg.
- Fatty-acid_metabolism_disorder wikiPageWikiLinkText "Fatty-acid metabolism disorder".
- Fatty-acid_metabolism_disorder wikiPageWikiLinkText "fatty acid oxidation disorder".
- Fatty-acid_metabolism_disorder wikiPageWikiLinkText "fatty-acid metabolism disorder".
- Fatty-acid_metabolism_disorder wikiPageWikiLinkText "fatty-acid oxidation disorders (FOD)".
- Fatty-acid_metabolism_disorder caption "Acyl-CoA, one of the compounds involved in fatty acid metabolism".
- Fatty-acid_metabolism_disorder icd "-".
- Fatty-acid_metabolism_disorder icd "277.81".
- Fatty-acid_metabolism_disorder icd "277.85".
- Fatty-acid_metabolism_disorder icd "E71.3".
- Fatty-acid_metabolism_disorder name "Fatty-acid metabolism disorder".
- Fatty-acid_metabolism_disorder wikiPageUsesTemplate Template:Fatty-acid_metabolism_disorders.
- Fatty-acid_metabolism_disorder wikiPageUsesTemplate Template:Infobox_Disease.
- Fatty-acid_metabolism_disorder wikiPageUsesTemplate Template:Reflist.
- Fatty-acid_metabolism_disorder subject Category:Autosomal_recessive_disorders.
- Fatty-acid_metabolism_disorder subject Category:Fatty-acid_metabolism_disorders.
- Fatty-acid_metabolism_disorder type Disorder.
- Fatty-acid_metabolism_disorder type Error.
- Fatty-acid_metabolism_disorder comment "A broad classification for genetic disorders that result from an inability of the body to produce or utilize one enzyme that is required to oxidize fatty acids. The enzyme can be missing or improperly constructed, resulting in it not working. This leaves the body unable to produce energy within the liver and muscles from fatty acid sources.The body's primary source of energy is glucose; however, when all the glucose in the body has been expended, a normal body digests fats.".
- Fatty-acid_metabolism_disorder label "Fatty-acid metabolism disorder".
- Fatty-acid_metabolism_disorder sameAs Q5437988.
- Fatty-acid_metabolism_disorder sameAs m.05p0f0y.
- Fatty-acid_metabolism_disorder sameAs Q5437988.
- Fatty-acid_metabolism_disorder wasDerivedFrom Fatty-acid_metabolism_disorder?oldid=678814116.
- Fatty-acid_metabolism_disorder depiction Acyl-CoA2.svg.
- Fatty-acid_metabolism_disorder isPrimaryTopicOf Fatty-acid_metabolism_disorder.