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- Familial_aortic_dissection abstract "Familial aortic dissection or FAD refers to the splitting of the wall of the aorta in either the arch, ascending or descending portions. FAD is thought to be passed down as an autosomal dominant disease and once inherited will result in dissection of the aorta, and dissecting aneurysm of the aorta, or rarely aortic or arterial dilation at a young age. Dissection refers to the actual tearing open of the aorta. However, the exact gene(s) involved has not yet been identified. It can occur in the absence of clinical features of Marfan syndrome and of systemic hypertension. Over time this weakness, along with systolic pressure, results in a tear in the aortic intima layer thus allowing blood to enter between the layers of tissue and cause further tearing. Eventually complete rupture of the aorta occurs and the pleural cavity fills with blood. Warning signs include chest pain, ischemia, and hemorrhaging in the chest cavity. This condition, unless found and treated early, usually results in death. Immediate surgery is the best prognosis in most cases. FAD is not to be confused with PAU (penetrating atherosclerotic ulcers) and IMH (intramural hematoma), both of which present in ways similar to that of familial aortic dissection.".
- Familial_aortic_dissection wikiPageID "21857803".
- Familial_aortic_dissection wikiPageLength "17083".
- Familial_aortic_dissection wikiPageOutDegree "45".
- Familial_aortic_dissection wikiPageRevisionID "689967737".
- Familial_aortic_dissection wikiPageWikiLink Actin.
- Familial_aortic_dissection wikiPageWikiLink Aneurysm.
- Familial_aortic_dissection wikiPageWikiLink Antihypertensive_drug.
- Familial_aortic_dissection wikiPageWikiLink Aorta.
- Familial_aortic_dissection wikiPageWikiLink Arteriosclerosis.
- Familial_aortic_dissection wikiPageWikiLink Beta_blocker.
- Familial_aortic_dissection wikiPageWikiLink Biomarker.
- Familial_aortic_dissection wikiPageWikiLink Bleeding.
- Familial_aortic_dissection wikiPageWikiLink Blood_pressure.
- Familial_aortic_dissection wikiPageWikiLink CT_scan.
- Familial_aortic_dissection wikiPageWikiLink Category:Vascular_diseases.
- Familial_aortic_dissection wikiPageWikiLink Coronary_artery_bypass_surgery.
- Familial_aortic_dissection wikiPageWikiLink Disease.
- Familial_aortic_dissection wikiPageWikiLink Dissection.
- Familial_aortic_dissection wikiPageWikiLink Dominance_(genetics).
- Familial_aortic_dissection wikiPageWikiLink Echocardiography.
- Familial_aortic_dissection wikiPageWikiLink Ehlers–Danlos_syndrome.
- Familial_aortic_dissection wikiPageWikiLink Epinephrine.
- Familial_aortic_dissection wikiPageWikiLink Heart_failure.
- Familial_aortic_dissection wikiPageWikiLink Heart_valve.
- Familial_aortic_dissection wikiPageWikiLink Hematoma.
- Familial_aortic_dissection wikiPageWikiLink Hypertension.
- Familial_aortic_dissection wikiPageWikiLink Intravenous_therapy.
- Familial_aortic_dissection wikiPageWikiLink Ischemia.
- Familial_aortic_dissection wikiPageWikiLink Lumen_(anatomy).
- Familial_aortic_dissection wikiPageWikiLink Magnetic_resonance_imaging.
- Familial_aortic_dissection wikiPageWikiLink Marfan_syndrome.
- Familial_aortic_dissection wikiPageWikiLink Metalloproteinase.
- Familial_aortic_dissection wikiPageWikiLink Myosin.
- Familial_aortic_dissection wikiPageWikiLink Penetrance.
- Familial_aortic_dissection wikiPageWikiLink Penetrating_atherosclerotic_ulcer.
- Familial_aortic_dissection wikiPageWikiLink Pericardium.
- Familial_aortic_dissection wikiPageWikiLink Pleural_cavity.
- Familial_aortic_dissection wikiPageWikiLink Protein_isoform.
- Familial_aortic_dissection wikiPageWikiLink Smooth_muscle_tissue.
- Familial_aortic_dissection wikiPageWikiLink Sodium_nitroprusside.
- Familial_aortic_dissection wikiPageWikiLink Tunica_intima.
- Familial_aortic_dissection wikiPageWikiLink Vasa_vasorum.
- Familial_aortic_dissection wikiPageWikiLinkText "Familial aortic dissection".
- Familial_aortic_dissection wikiPageUsesTemplate Template:Reflist.
- Familial_aortic_dissection wikiPageUsesTemplate Template:Vascular_diseases.
- Familial_aortic_dissection subject Category:Vascular_diseases.
- Familial_aortic_dissection comment "Familial aortic dissection or FAD refers to the splitting of the wall of the aorta in either the arch, ascending or descending portions. FAD is thought to be passed down as an autosomal dominant disease and once inherited will result in dissection of the aorta, and dissecting aneurysm of the aorta, or rarely aortic or arterial dilation at a young age. Dissection refers to the actual tearing open of the aorta. However, the exact gene(s) involved has not yet been identified.".
- Familial_aortic_dissection label "Familial aortic dissection".
- Familial_aortic_dissection sameAs Q5432930.
- Familial_aortic_dissection sameAs m.05p7qb1.
- Familial_aortic_dissection sameAs Q5432930.
- Familial_aortic_dissection wasDerivedFrom Familial_aortic_dissection?oldid=689967737.
- Familial_aortic_dissection isPrimaryTopicOf Familial_aortic_dissection.