Matches in DBpedia 2016-04 for { <http://dbpedia.org/resource/Cystic_fibrosis> ?p ?o }
- Cystic_fibrosis abstract "Cystic fibrosis (CF) is a genetic disorder that affects mostly the lungs but also the pancreas, liver, kidneys, and intestine. Long-term issues include difficulty breathing and coughing up mucus as a result of frequent lung infections. Other signs and symptoms include sinus infections, poor growth, fatty stool, clubbing of the fingers and toes, and infertility in males among others. Different people may have different degrees of symptoms.CF is inherited in an autosomal recessive manner. It is caused by the presence of mutations in both copies of the gene for the cystic fibrosis transmembrane conductance regulator (CFTR) protein. Those with a single working copy are carriers and otherwise mostly normal. CFTR is involved in production of sweat, digestive fluids, and mucus. When CFTR is not functional, secretions which are usually thin instead become thick. The condition is diagnosed by a sweat test and genetic testing. Screening of infants at birth takes place in some areas of the world.There is no cure for cystic fibrosis. Lung infections are treated with antibiotics which may be given intravenously, inhaled, or by mouth. Sometimes the antibiotic azithromycin is used long term. Inhaled hypertonic saline and salbutamol may also be useful. Lung transplantation may be an option if lung function continues to worsen. Pancreatic enzyme replacement and fat-soluble vitamin supplementation are important, especially in the young. While not well supported by evidence, many people use airway clearance techniques such as chest physiotherapy. The average life expectancy is between 42 and 50 years in the developed world. Lung problems are responsible for death in 80% of people with cystic fibrosis.CF is most common among people of Northern European ancestry and affects about one out of every 3,000 newborns. About one in 25 people are carriers. It is least common in Africans and Asians. It was first recognized as a specific disease by Dorothy Andersen in 1938, with descriptions that fit the condition occurring at least as far back as 1595. The name cystic fibrosis refers to the characteristic fibrosis and cysts that form within the pancreas.".
- Cystic_fibrosis icd10 "E84".
- Cystic_fibrosis icd9 "277.0".
- Cystic_fibrosis meshId "D003550".
- Cystic_fibrosis omim "219700".
- Cystic_fibrosis thumbnail ClubbingCF.JPG?width=300.
- Cystic_fibrosis wikiPageExternalLink cf-week.
- Cystic_fibrosis wikiPageExternalLink results.
- Cystic_fibrosis wikiPageExternalLink app.
- Cystic_fibrosis wikiPageID "50601".
- Cystic_fibrosis wikiPageLength "99002".
- Cystic_fibrosis wikiPageOutDegree "364".
- Cystic_fibrosis wikiPageRevisionID "707197442".
- Cystic_fibrosis wikiPageWikiLink 65_Redroses.
- Cystic_fibrosis wikiPageWikiLink ATP-binding_cassette_transporter.
- Cystic_fibrosis wikiPageWikiLink ATP_hydrolysis.
- Cystic_fibrosis wikiPageWikiLink Acrophialophora_fusispora.
- Cystic_fibrosis wikiPageWikiLink Adenosine_triphosphate.
- Cystic_fibrosis wikiPageWikiLink Adverse_drug_reaction.
- Cystic_fibrosis wikiPageWikiLink Africa.
- Cystic_fibrosis wikiPageWikiLink Airway_clearance_technique.
- Cystic_fibrosis wikiPageWikiLink Allergic_bronchopulmonary_aspergillosis.
- Cystic_fibrosis wikiPageWikiLink Alpha_helix.
- Cystic_fibrosis wikiPageWikiLink Amenorrhoea.
- Cystic_fibrosis wikiPageWikiLink American_Congress_of_Obstetricians_and_Gynecologists.
- Cystic_fibrosis wikiPageWikiLink Amino_acid.
- Cystic_fibrosis wikiPageWikiLink Aminoglycoside.
- Cystic_fibrosis wikiPageWikiLink Amniocentesis.
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- Cystic_fibrosis wikiPageWikiLink Anti-diabetic_medication.
- Cystic_fibrosis wikiPageWikiLink Antibiotics.
- Cystic_fibrosis wikiPageWikiLink Antimicrobial_resistance.
- Cystic_fibrosis wikiPageWikiLink Antioxidant.
- Cystic_fibrosis wikiPageWikiLink Asian_people.
- Cystic_fibrosis wikiPageWikiLink Aspergillus_flavus.
- Cystic_fibrosis wikiPageWikiLink Aspergillus_fumigatus.
- Cystic_fibrosis wikiPageWikiLink Aspergillus_nidulans.
- Cystic_fibrosis wikiPageWikiLink Aspergillus_terreus.
- Cystic_fibrosis wikiPageWikiLink Assisted_reproductive_technology.
- Cystic_fibrosis wikiPageWikiLink Ataluren.
- Cystic_fibrosis wikiPageWikiLink Atherosclerosis.
- Cystic_fibrosis wikiPageWikiLink Azithromycin.
- Cystic_fibrosis wikiPageWikiLink Azoospermia.
- Cystic_fibrosis wikiPageWikiLink Aztreonam.
- Cystic_fibrosis wikiPageWikiLink Bacteria.
- Cystic_fibrosis wikiPageWikiLink Base_pair.
- Cystic_fibrosis wikiPageWikiLink Bile.
- Cystic_fibrosis wikiPageWikiLink Bile_duct.
- Cystic_fibrosis wikiPageWikiLink Bilevel_positive_airway_pressure.
- Cystic_fibrosis wikiPageWikiLink Binding_site.
- Cystic_fibrosis wikiPageWikiLink Biofilm.
- Cystic_fibrosis wikiPageWikiLink Biphasic_cuirass_ventilation.
- Cystic_fibrosis wikiPageWikiLink Bisphosphonate.
- Cystic_fibrosis wikiPageWikiLink Blood_pressure.
- Cystic_fibrosis wikiPageWikiLink Bone_fracture.
- Cystic_fibrosis wikiPageWikiLink Bowel_obstruction.
- Cystic_fibrosis wikiPageWikiLink Breast_milk.
- Cystic_fibrosis wikiPageWikiLink Breathing_for_a_Living.
- Cystic_fibrosis wikiPageWikiLink Bronchiectasis.
- Cystic_fibrosis wikiPageWikiLink Burkholderia_cepacia_complex.
- Cystic_fibrosis wikiPageWikiLink C-terminus.
- Cystic_fibrosis wikiPageWikiLink Calcium.
- Cystic_fibrosis wikiPageWikiLink Calorie.
- Cystic_fibrosis wikiPageWikiLink Canada.
- Cystic_fibrosis wikiPageWikiLink Candida_albicans.
- Cystic_fibrosis wikiPageWikiLink Carl_von_Rokitansky.
- Cystic_fibrosis wikiPageWikiLink Category:Autosomal_recessive_disorders.
- Cystic_fibrosis wikiPageWikiLink Category:Channelopathy.
- Cystic_fibrosis wikiPageWikiLink Category:Congenital_disorders.
- Cystic_fibrosis wikiPageWikiLink Category:Cystic_fibrosis.
- Cystic_fibrosis wikiPageWikiLink Category:Lung_disorders.
- Cystic_fibrosis wikiPageWikiLink Category:Pancreas_disorders.
- Cystic_fibrosis wikiPageWikiLink Category:Pediatrics.
- Cystic_fibrosis wikiPageWikiLink Category:RTT.
- Cystic_fibrosis wikiPageWikiLink Category:Rare_diseases.
- Cystic_fibrosis wikiPageWikiLink Category:Steatorrhea-related_diseases.
- Cystic_fibrosis wikiPageWikiLink Cell_(biology).
- Cystic_fibrosis wikiPageWikiLink Cell_membrane.
- Cystic_fibrosis wikiPageWikiLink Chest_physiotherapy.
- Cystic_fibrosis wikiPageWikiLink Chest_wall_oscillation.
- Cystic_fibrosis wikiPageWikiLink Chloride.
- Cystic_fibrosis wikiPageWikiLink Cholera_toxin.
- Cystic_fibrosis wikiPageWikiLink Chorionic_villus_sampling.
- Cystic_fibrosis wikiPageWikiLink Chromosome_7_(human).
- Cystic_fibrosis wikiPageWikiLink Chromosome_jumping.
- Cystic_fibrosis wikiPageWikiLink Chronic_pancreatitis.
- Cystic_fibrosis wikiPageWikiLink Cilium.
- Cystic_fibrosis wikiPageWikiLink Cirrhosis.
- Cystic_fibrosis wikiPageWikiLink Classical_genetics.
- Cystic_fibrosis wikiPageWikiLink Clinical_trial.
- Cystic_fibrosis wikiPageWikiLink Coagulation.
- Cystic_fibrosis wikiPageWikiLink Coagulopathy.
- Cystic_fibrosis wikiPageWikiLink Coeliac_disease.
- Cystic_fibrosis wikiPageWikiLink Colistin.
- Cystic_fibrosis wikiPageWikiLink Congenital_absence_of_the_vas_deferens.
- Cystic_fibrosis wikiPageWikiLink Constipation.
- Cystic_fibrosis wikiPageWikiLink Coronary_artery_disease.
- Cystic_fibrosis wikiPageWikiLink Corticosteroid.
- Cystic_fibrosis wikiPageWikiLink Cyst.
- Cystic_fibrosis wikiPageWikiLink Cystic_fibrosis-related_diabetes.