Matches in DBpedia 2015-10 for { <http://dbpedia.org/resource/Methylmalonyl-CoA_mutase> ?p ?o }
- Methylmalonyl-CoA_mutase abstract "Methylmalonyl Coenzyme A mutase, also known as MCM is an enzyme that catalyzes the isomerization of methylmalonyl-CoA to succinyl-CoA and it is involved in key metabolic pathways. It requires a vitamin B12-derived prosthetic group, adenosylcobalamin (commonly referred to as AdoCbl), to function.Methylmalonyl-CoA mutase was first identified in rat liver and sheep kidney in 1955. In its latent form, it is 750 amino acids in length. Upon entry to the mitochondria, the 32 amino acid mitochondrial leader sequence at the N-terminus of the protein is cleaved, forming the fully processed monomer. The monomers then associate into homodimers, and bind AdoCbl (one for each monomer active site) to form the final, active holoenzyme form.The processing protein, MMAA protein, fills the important role of aiding cofactor loading and exchange. MMAA protein favors association with the MCM apoenzyme, and allows for the transfer of the AdoCbl cofactor to the enzyme active site. Furthermore, if the bound AdoCbl accrues oxidative damage during normal functioning, MMAA protein fosters exchange of the damaged cofactor for a new AdoCbl via a GTP-reliant pathway.Methylmalonyl-CoA mutase is expressed in high concentrations in the kidney, in intermediate concentrations in the heart, ovaries, brain, muscle, and liver, and in low concentrations in the spleen. The enzyme can be found all throughout the central nervous system (CNS).".
- Methylmalonyl-CoA_mutase entrezgene "4594".
- Methylmalonyl-CoA_mutase thumbnail L-methylmalonyl-CoA.png?width=300.
- Methylmalonyl-CoA_mutase wikiPageExternalLink br.fcgi?book=gene&part=mma.
- Methylmalonyl-CoA_mutase wikiPageID "5913741".
- Methylmalonyl-CoA_mutase wikiPageLength "21765".
- Methylmalonyl-CoA_mutase wikiPageOutDegree "70".
- Methylmalonyl-CoA_mutase wikiPageRevisionID "678963708".
- Methylmalonyl-CoA_mutase wikiPageWikiLink Adenosylcobalamin.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Apoenzyme.
- Methylmalonyl-CoA_mutase wikiPageWikiLink BCG_vaccine.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Bovine_tuberculosis.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Brain.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Branched-chain_amino_acid.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Branched-chain_amino_acids.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Category:Human_proteins.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Central_nervous_system.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Cholesterol.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Chromosome.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Citric_acid_cycle.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Cobalt.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Cobamamide.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Cofactor_(biochemistry).
- Methylmalonyl-CoA_mutase wikiPageWikiLink Corrin.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Corrin_ring.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Enzyme.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Fatty_acid.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Fatty_acids.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Free_radical.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Glutamate.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Glutamic_acid.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Guanosine_triphosphate.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Heart.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Heterolysis_(chemistry).
- Methylmalonyl-CoA_mutase wikiPageWikiLink Histidine.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Holoenzyme.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Homolysis_(chemistry).
- Methylmalonyl-CoA_mutase wikiPageWikiLink Isoleucine.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Isomerase.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Kidney.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Kidney_disease.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Kidney_transplant.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Kidney_transplantation.
- Methylmalonyl-CoA_mutase wikiPageWikiLink L-methylmalonyl-CoA.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Liver.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Liver_transplant.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Liver_transplantation.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Livestock.
- Methylmalonyl-CoA_mutase wikiPageWikiLink MMAA.
- Methylmalonyl-CoA_mutase wikiPageWikiLink MMAB.
- Methylmalonyl-CoA_mutase wikiPageWikiLink MMACHC.
- Methylmalonyl-CoA_mutase wikiPageWikiLink MMADHC.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Methionine.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Methylmalonic_acidemia.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Methylmalonyl-CoA.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Methylmalonyl-CoA_mutase_deficiency.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Missense_mutation.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Missense_mutations.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Murinae.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Murine.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Muscle.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Mycobacterium_bovis.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Nonsense_mutation.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Nonsense_mutations.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Ovaries.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Ovary.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Propionyl-CoA.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Prosthetic_group.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Radical_(chemistry).
- Methylmalonyl-CoA_mutase wikiPageWikiLink Rat.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Renal_disease.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Ribose.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Sheep.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Spleen.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Succinyl-CoA.
- Methylmalonyl-CoA_mutase wikiPageWikiLink TCA_cycle.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Threonine.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Thymine.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Tuberculosis.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Tyrosine.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Valine.
- Methylmalonyl-CoA_mutase wikiPageWikiLink Vitamin_B12.
- Methylmalonyl-CoA_mutase wikiPageWikiLink File:Active_site_MCM_colors.png.
- Methylmalonyl-CoA_mutase wikiPageWikiLink File:MUT.png.
- Methylmalonyl-CoA_mutase wikiPageWikiLinkText "MUT enzyme".
- Methylmalonyl-CoA_mutase wikiPageWikiLinkText "MUT".
- Methylmalonyl-CoA_mutase wikiPageWikiLinkText "Methylmalonyl Coenzyme A mutase".
- Methylmalonyl-CoA_mutase wikiPageWikiLinkText "Methylmalonyl-CoA mutase".
- Methylmalonyl-CoA_mutase wikiPageWikiLinkText "methylmalonyl coenzyme A mutase".
- Methylmalonyl-CoA_mutase wikiPageWikiLinkText "methylmalonyl-CoA mutase".
- Methylmalonyl-CoA_mutase casNumber "9023".
- Methylmalonyl-CoA_mutase ecNumber "5.4".
- Methylmalonyl-CoA_mutase forwardEnzyme "methylmalonyl-CoA mutase".
- Methylmalonyl-CoA_mutase goCode "4494".
- Methylmalonyl-CoA_mutase hasPhotoCollection Methylmalonyl-CoA_mutase.
- Methylmalonyl-CoA_mutase iubmbEcNumber "5".
- Methylmalonyl-CoA_mutase name "methylmalonyl-CoA mutase".
- Methylmalonyl-CoA_mutase product Succinyl-CoA.
- Methylmalonyl-CoA_mutase productImage "succinyl-CoA.png 200px".
- Methylmalonyl-CoA_mutase reverse)_ "reversible".