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- Diencephalic_syndrome abstract "Diencephalic syndrome, diencephalic syndrome of emaciation or Russell's syndrome is a rare neurological disorder seen in infants and children and characterised by failure to thrive and severe emaciation despite normal or slightly decreased caloric intake, locomotor hyperactivity, and euphoria. Less commonly it may involve skin pallor without anaemia, hypoglycaemia, and hypotension. The syndrome is a rare but potentially fatal cause of failure to thrive in children. Failure to thrive presents on average at 7 months of age. Of note the syndrome is not associated with developmental delay. There may be associated hydrocephalus. Diencephalic syndrome was first described by Russell in 1951. It is usually caused by a brain tumor such as a low-grade glioma or astrocytoma located in the hypothalamic-optic chiasmatic region. It is not yet understood how diencephalic syndrome causes the effects on appetite and metabolism which are seen, though inappropraitely high growth hormone release has been proposed, as has excessive β-lipotropin secretion and overall increased metabolic demand. It is treated with nutritional optimisation while the underlying lesion is treated with chemotherapy, surgery or radiotherapy.".
- Diencephalic_syndrome thumbnail 1310_Diencephalon.jpg?width=300.
- Diencephalic_syndrome wikiPageID "47294362".
- Diencephalic_syndrome wikiPageLength "3499".
- Diencephalic_syndrome wikiPageOutDegree "20".
- Diencephalic_syndrome wikiPageRevisionID "676842530".
- Diencephalic_syndrome wikiPageWikiLink Anaemia.
- Diencephalic_syndrome wikiPageWikiLink Anemia.
- Diencephalic_syndrome wikiPageWikiLink Astrocytoma.
- Diencephalic_syndrome wikiPageWikiLink Category:Neurological_disorders.
- Diencephalic_syndrome wikiPageWikiLink Category:Neurological_disorders_in_children.
- Diencephalic_syndrome wikiPageWikiLink Category:Oncology.
- Diencephalic_syndrome wikiPageWikiLink Category:Syndromes.
- Diencephalic_syndrome wikiPageWikiLink Chemotherapy.
- Diencephalic_syndrome wikiPageWikiLink Emaciation.
- Diencephalic_syndrome wikiPageWikiLink Failure_to_thrive.
- Diencephalic_syndrome wikiPageWikiLink Glioma.
- Diencephalic_syndrome wikiPageWikiLink Growth_hormone.
- Diencephalic_syndrome wikiPageWikiLink Hydrocephalus.
- Diencephalic_syndrome wikiPageWikiLink Hypoglycaemia.
- Diencephalic_syndrome wikiPageWikiLink Hypoglycemia.
- Diencephalic_syndrome wikiPageWikiLink Hypotension.
- Diencephalic_syndrome wikiPageWikiLink Hypothalamus.
- Diencephalic_syndrome wikiPageWikiLink Lipotropin.
- Diencephalic_syndrome wikiPageWikiLink Optic_chiasm.
- Diencephalic_syndrome wikiPageWikiLink Radiation_therapy.
- Diencephalic_syndrome wikiPageWikiLink Radiotherapy.
- Diencephalic_syndrome wikiPageWikiLink Surgery.
- Diencephalic_syndrome wikiPageWikiLink File:1310_Diencephalon.jpg.
- Diencephalic_syndrome wikiPageWikiLinkText "Diencephalic syndrome".
- Diencephalic_syndrome hasPhotoCollection Diencephalic_syndrome.
- Diencephalic_syndrome wikiPageUsesTemplate Template:CNS_diseases_of_the_nervous_system.
- Diencephalic_syndrome wikiPageUsesTemplate Template:Reflist.
- Diencephalic_syndrome subject Category:Neurological_disorders.
- Diencephalic_syndrome subject Category:Neurological_disorders_in_children.
- Diencephalic_syndrome subject Category:Oncology.
- Diencephalic_syndrome subject Category:Syndromes.
- Diencephalic_syndrome hypernym Disorder.
- Diencephalic_syndrome type Disease.
- Diencephalic_syndrome comment "Diencephalic syndrome, diencephalic syndrome of emaciation or Russell's syndrome is a rare neurological disorder seen in infants and children and characterised by failure to thrive and severe emaciation despite normal or slightly decreased caloric intake, locomotor hyperactivity, and euphoria. Less commonly it may involve skin pallor without anaemia, hypoglycaemia, and hypotension. The syndrome is a rare but potentially fatal cause of failure to thrive in children.".
- Diencephalic_syndrome label "Diencephalic syndrome".
- Diencephalic_syndrome wasDerivedFrom Diencephalic_syndrome?oldid=676842530.
- Diencephalic_syndrome depiction 1310_Diencephalon.jpg.
- Diencephalic_syndrome isPrimaryTopicOf Diencephalic_syndrome.