Matches in DBpedia 2015-10 for { <http://dbpedia.org/resource/Degos_disease> ?p ?o }
- Degos_disease abstract "Degos disease (also called malignant atrophic papulosis) is a rare vasculopathy that affects the lining of the medium and small veins and arteries, resulting in occlusion (blockage of the vessel) and tissue infarction.The blood vessels affected include those supplying the skin, gastrointestinal tract, and central nervous system. This can result in bowel ischemia (mesenteric ischemia or ischemic colitis), chronic skin lesions, ocular lesions, strokes, spinal lesions, mononeuritis multiplex, epilepsy, headaches or cognitive disorders. Pleural or pericardial effusions are also reported.There are fewer than 50 living patients at present known worldwide, and fewer than 200 reported in medical literature.The outcome of this disease can be fatal with a median survival of 2 to 3 years, although some appear to have a benign form (Degos acanthoma) which affects only the skin. Laparoscopy may be an effective means of screening those with cutaneous lesions to determine if systemic disease is present. Treatment options are limited, and until recently consisted mainly of antiplatelet drugs or anticoagulants or immunosuppressants with few reports of prolonged survival. More recently eculizumab and treprostinil have been employed. Response to eculizumab is often immediate and dramatic, but has been of limited duration in all so treated. Treprostinil use has been reported to result in clearing of gastrointestinal and CNS findings as well as clearing of cutaneous lesions, but reports are limited. Treprostinil may be more effective than other vasodilators because it may also increase the population of circulating endothelial cells, allowing angiogenesis.There are suggestions that Degos disease is not a separate disorder, but the final result of several vascular systemic disorders.".
- Degos_disease icd9 "447.8".
- Degos_disease meshId "D054853".
- Degos_disease omim "602248".
- Degos_disease thumbnail Degos-disease.jpg?width=300.
- Degos_disease wikiPageExternalLink 13.
- Degos_disease wikiPageExternalLink openurl?genre=article&sid=nlm:pubmed&issn=0307-6938&date=2007&volume=32&issue=5&spage=483.
- Degos_disease wikiPageExternalLink www.degosdisease.com.
- Degos_disease wikiPageID "20170906".
- Degos_disease wikiPageID "30391047".
- Degos_disease wikiPageID "4112395".
- Degos_disease wikiPageLength "27".
- Degos_disease wikiPageLength "7847".
- Degos_disease wikiPageOutDegree "1".
- Degos_disease wikiPageOutDegree "37".
- Degos_disease wikiPageRedirects Degos_disease.
- Degos_disease wikiPageRevisionID "251188057".
- Degos_disease wikiPageRevisionID "406954782".
- Degos_disease wikiPageRevisionID "664704796".
- Degos_disease wikiPageWikiLink Acanthoma.
- Degos_disease wikiPageWikiLink Albany_Medical_College.
- Degos_disease wikiPageWikiLink Alexion_Pharmaceuticals.
- Degos_disease wikiPageWikiLink American_College_of_Rheumatology.
- Degos_disease wikiPageWikiLink Angiogenesis.
- Degos_disease wikiPageWikiLink Anticoagulant.
- Degos_disease wikiPageWikiLink Antiplatelet_drug.
- Degos_disease wikiPageWikiLink Arteries.
- Degos_disease wikiPageWikiLink Artery.
- Degos_disease wikiPageWikiLink Category:Rare_diseases.
- Degos_disease wikiPageWikiLink Category:Vascular-related_cutaneous_conditions.
- Degos_disease wikiPageWikiLink Category:Vascular_diseases.
- Degos_disease wikiPageWikiLink Central_nervous_system.
- Degos_disease wikiPageWikiLink Cognitive_disorder.
- Degos_disease wikiPageWikiLink Degos_disease.
- Degos_disease wikiPageWikiLink Digestion.
- Degos_disease wikiPageWikiLink Eculizumab.
- Degos_disease wikiPageWikiLink Epilepsy.
- Degos_disease wikiPageWikiLink Food_and_Drug_Administration.
- Degos_disease wikiPageWikiLink Gastrointestinal_tract.
- Degos_disease wikiPageWikiLink Headache.
- Degos_disease wikiPageWikiLink Immunosuppressant.
- Degos_disease wikiPageWikiLink Immunosuppression.
- Degos_disease wikiPageWikiLink Infarction.
- Degos_disease wikiPageWikiLink Ischemic_colitis.
- Degos_disease wikiPageWikiLink Massachusetts_General_Hospital.
- Degos_disease wikiPageWikiLink Mesenteric_ischemia.
- Degos_disease wikiPageWikiLink Mononeuritis_multiplex.
- Degos_disease wikiPageWikiLink Paroxysmal_nocturnal_hemoglobinuria.
- Degos_disease wikiPageWikiLink Pericardial_effusion.
- Degos_disease wikiPageWikiLink Peripheral_neuropathy.
- Degos_disease wikiPageWikiLink Pleural_effusion.
- Degos_disease wikiPageWikiLink Robert_Degos.
- Degos_disease wikiPageWikiLink Skin.
- Degos_disease wikiPageWikiLink Stroke.
- Degos_disease wikiPageWikiLink Treprostinil.
- Degos_disease wikiPageWikiLink Vascular_occlusion.
- Degos_disease wikiPageWikiLink Vasculitis.
- Degos_disease wikiPageWikiLink Vasculopathies.
- Degos_disease wikiPageWikiLink Vein.
- Degos_disease wikiPageWikiLinkText "Dego's disease".
- Degos_disease wikiPageWikiLinkText "Degos disease".
- Degos_disease wikiPageWikiLinkText "degos disease".
- Degos_disease caption "Skin lesions in a person with Degos disease".
- Degos_disease diseasesdb "29425".
- Degos_disease emedicinesubj "derm".
- Degos_disease emedicinetopic "931".
- Degos_disease hasPhotoCollection Degos_disease.
- Degos_disease icd "447.8".
- Degos_disease meshid "D054853".
- Degos_disease name "Degos disease".
- Degos_disease omim "602248".
- Degos_disease wikiPageUsesTemplate Template:Cite_journal.
- Degos_disease wikiPageUsesTemplate Template:Infobox_disease.
- Degos_disease wikiPageUsesTemplate Template:Refbegin.
- Degos_disease wikiPageUsesTemplate Template:Refend.
- Degos_disease wikiPageUsesTemplate Template:Reflist.
- Degos_disease wikiPageUsesTemplate Template:Vascular_diseases.
- Degos_disease subject Category:Rare_diseases.
- Degos_disease subject Category:Vascular-related_cutaneous_conditions.
- Degos_disease subject Category:Vascular_diseases.
- Degos_disease hypernym Vasculopathy.
- Degos_disease type Disease.
- Degos_disease type Thing.
- Degos_disease type Q12136.
- Degos_disease comment "Degos disease (also called malignant atrophic papulosis) is a rare vasculopathy that affects the lining of the medium and small veins and arteries, resulting in occlusion (blockage of the vessel) and tissue infarction.The blood vessels affected include those supplying the skin, gastrointestinal tract, and central nervous system.".
- Degos_disease label "Dego's disease".
- Degos_disease label "Degos disease".
- Degos_disease label "Degos' disease".
- Degos_disease sameAs كثرة_الحطاطات_الضمورية_الخبيثة.
- Degos_disease sameAs Category:Degos_disease.
- Degos_disease sameAs Degosova_nemoc.
- Degos_disease sameAs Degos-Syndrom.
- Degos_disease sameAs Enfermedad_de_Degos.
- Degos_disease sameAs Maladie_de_Degos.
- Degos_disease sameAs Malattia_di_Degos.
- Degos_disease sameAs Choroba_Degosa.
- Degos_disease sameAs Papulose_atrofiante_maligna.
- Degos_disease sameAs m.0bjrxf.
- Degos_disease sameAs Q911136.
- Degos_disease sameAs Q911136.